Childhood Kidney Diseases

Korean Society of Pediatric Nephrology (대한소아신장학회)
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Nutcracker Syndrome in Siblings

형제에서 발생한 호두까기 증후군 증례보고 및 문헌 고찰

  • Lee, Na-Ra (Department of Pediatrics, College of Medicine, Korea University) ;
  • Oh, Jung-Min (Department of Pediatrics, College of Medicine, Korea University) ;
  • Yim, Hyung-Eun (Department of Pediatrics, College of Medicine, Korea University) ;
  • Yoo, Kee-Hwan (Department of Pediatrics, College of Medicine, Korea University) ;
  • Hong, Young-Sook (Department of Pediatrics, College of Medicine, Korea University) ;
  • Lee, Joo-Won (Department of Pediatrics, College of Medicine, Korea University)
  • 이나라 (고려대학교 의과대학 소아과학교실) ;
  • 오정민 (고려대학교 의과대학 소아과학교실) ;
  • 임형은 (고려대학교 의과대학 소아과학교실) ;
  • 유기환 (고려대학교 의과대학 소아과학교실) ;
  • 홍영숙 (고려대학교 의과대학 소아과학교실) ;
  • 이주원 (고려대학교 의과대학 소아과학교실)
  • Received : 2010.09.14
  • Accepted : 2010.10.18
  • Published : 2010.10.31
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Abstract

Nutcracker syndrome refers to the compression of the left renal vein between the abdominal aorta and superior mesenteric artery which can lead to renal vein hypertension. Patients can present with hematuria, proteinuria, dysuria or abdominal pain. In diagnosing the nutcracker syndrome, measurement of the peak velocity ratio of aorto-mesenteric border versus renal hilum by Doppler sonography is useful. Currently, there are few reports about the genetic correlation in this syndrome. We report two cases of the nutcracker syndrome found in male siblings with hematuria.

호두까기 증후군은 대동맥과 상장간막 동맥 사이에 좌신 정맥이 압박되어 혈뇨나 단백뇨가 보이는 임상 증후군으로 그 유전성에 대해서는 알려져 있는 바가 없다. 저자들은 무증상 혈뇨를 주소로 내원한 형제에게 모두 도플러 초음파로 진단된 호두까기 증후군을 접하였기에 간단한 문헌 고찰과 함께 보고하는 바이다.

Keywords

References

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