Clinical and Experimental Pediatrics

대한소아청소년과학회 (The Korean Pediatric Society)
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심한 폐동맥 고혈압을 동반한 선천성 심장병 환자에서 수술 전후 Iloprost 효과

The effect of perioperative inhaled iloprost on congenital heart disease with severe pulmonary arterial hypertension

  • 김수남 (가천의과학대학교 길병원 소아과학교실) ;
  • 최덕영 (가천의과학대학교 길병원 소아과학교실)
  • Kim, Su Nam (Department of Pediatrics, Gil Hospital, Gachon University of Medicine) ;
  • Choi, Deok Young (Department of Pediatrics, Gil Hospital, Gachon University of Medicine)
  • 투고 : 2009.09.09
  • 심사 : 2009.10.27
  • 발행 : 2010.01.15
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초록

15년전 심방중격 결손증 진단을 받은 47세 남자 환자가 심도자 검사를 위해 입원하였다. 환자는 입술과 손톱에서 명확한 청색증을 보이고 있었으며 심한 폐동맥 고혈압을 나타내고 있었다. 본 환자는 지난 수년간 아이젠멩거 증후군으로 진단되어 대증적 치료만을 받아오고 있었다. 심도자 검사 후 환자는 흡입형 Iloprost 치료를 시작 하였으며 성공적으로 심방중격결손증 수술을 받을 수 있었다. 환자는 수술 후에도 치료를 지속하였다.

A 47-year-old male patient in whom atrial septal defect (ASD) had been diagnosed 15 years previously was admitted for cardiac catheterization. He had definite cyanotic lips and nail beds and severe pulmonary arterial hypertension (PAH). He had received medical treatment only for the last few years after being diagnosed with Eisenmenger syndrome. After cardiac catheterization, he received iloprost inhalation therapy pre and postoperation and was discharged after successful surgical closure of the ASD.

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참고문헌

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