Neonatal Medicine

The Korean Society of Neonatology (대한신생아학회)
권호 표지

A Case of Giant Congenital Melanocytic Nevi in a Neonate

신생아에서 발생한 거대 선천성 멜라닌세포 모반 1례

  • Cho, Seo-Eun (Department of Pediatrics, College of Medicine, Korea University) ;
  • Choi, Lim (Department of Pediatrics, College of Medicine, Korea University) ;
  • Park, Kyu-Hee (Department of Pediatrics, College of Medicine, Korea University) ;
  • Lee, Jang-Hoon (Department of Pediatrics, College of Medicine, Korea University) ;
  • Choi, Byung-Min (Department of Pediatrics, College of Medicine, Korea University) ;
  • Hong, Young-Sook (Department of Pediatrics, College of Medicine, Korea University) ;
  • Yoo, Kee-Hwan (Department of Pediatrics, College of Medicine, Korea University) ;
  • Lee, Joo-Won (Department of Pediatrics, College of Medicine, Korea University)
  • 조세은 (고려대학교 의과대학 소아과학교실) ;
  • 최림 (고려대학교 의과대학 소아과학교실) ;
  • 박규희 (고려대학교 의과대학 소아과학교실) ;
  • 이장훈 (고려대학교 의과대학 소아과학교실) ;
  • 최병민 (고려대학교 의과대학 소아과학교실) ;
  • 홍영숙 (고려대학교 의과대학 소아과학교실) ;
  • 유기환 (고려대학교 의과대학 소아과학교실) ;
  • 이주원 (고려대학교 의과대학 소아과학교실)
  • Published : 2010.05.31
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Abstract

Giant congenital melanocytic nevi are very rare, with an estimated incidence of 1 in 20,000 live births. They have a high risk of malignant melanoma transformation and neurological deficits such as neurocutaneous melanocytosis and epilepsy. Early evaluation, surgical intervention and careful long term follow up are recommended to monitor for malignant transformation. We report one case of giant congenital melanocytic nevi diagnosed at birth with the related literatures.

신생아에서 선천성 거대 멜라닌세포 모반은 드물게 발생하지만 악성 흑색종, 연수막멜라닌세포증, 간질과 같은 신경학적 결함의 발생 위험성이 높은 질환으로서 수술적 절제 및 장기적 추적관찰을 필요로 한다. 저자들은 출생시 부터 흉부의 선천성 거대 멜라닌세포 모반과 두경부 및 사지의 위성모반을 보인 여아 1례를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Keywords

References

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