Pediatric Gastroenterology, Hepatology & Nutrition

The Korean Society of Pediatric Gastroenterology, Hepatology and Nutrition (대한소아소화기영양학회)
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A Case of Hepatic Vein Thrombosis Associated with Ulcerative Colitis

궤양성 대장염에 동반된 간정맥 혈전증 1예

  • Kim, Joon-Sung (Department of Pediatrics, Ulsan University Hospital, University of Ulsan College of Medicine) ;
  • Kim, Kyung-Mo (Asan Medical Center, Seoul, University of Ulsan College of Medicine)
  • 김준성 (울산대학교 의과대학 울산대학교병원) ;
  • 김경모 (서울아산병원 소아청소년과)
  • Received : 2009.07.31
  • Accepted : 2009.08.27
  • Published : 2009.09.30
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Abstract

Patients with inflammatory bowel disease are known to have hypercoagulability and an increased risk for venous thromboembolism. The deep veins of the lower extremities and the pulmonary veins are the most common sites of thrombosis in ulcerative colitis. However, hepatic vein thrombosis (Budd-Chiari syndrome) is a very rare extra-intestinal complication of ulcerative colitis in children. We describe a case of hepatic vein thrombosis in a 15-year-old girl with ulcerative colitis who presented with abdominal pain and hematochezia. Doppler ultrasonography and an abdominal CT scan revealed the characteristic filling defects caused by large thrombi in both hepatic veins. These lesions were successfully treated with conventional management for ulcerative colitis and anticoagulation therapy.

저자들은 궤양성 대장염으로 진단되어 치료 중이던 15세 소아에서 발생한 간정맥 혈전증(Budd-Chiari 증후군) 1예를 경험하였기에 문헌고찰과 함께 보고한다. 간정맥 혈전증은 소아 궤양성 대장염의 매우 드문 혈관계 합병증으로 이환율과 사망률의 주요한 원인이 될 수 있으므로 진단과 치료에 보다 세심한 주의가 필요하다.

Keywords

References

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