Pediatric Gastroenterology, Hepatology & Nutrition

  • 제12권1호
  • /
  • Pages.57-63
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  • 2009
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  • 2234-8646(pISSN)
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  • 2234-8840(eISSN)
대한소아소화기영양학회 (The Korean Society of Pediatric Gastroenterology, Hepatology and Nutrition)
권호 표지

위 내 이물로 오인한 석회화 섬유 종양 1예

Calcifying Fibrous Tumor Mimicking a Foreign Body of the Stomach: A Case Report

  • 정지은 (대구가톨릭대학교 의과대학 소아과학교실) ;
  • 이경훈 (대구가톨릭대학교 의과대학 소아과학교실) ;
  • 성현정 (대구가톨릭대학교 의과대학 병리과학교실) ;
  • 조창호 (대구가톨릭대학교 의과대학 병리과학교실)
  • Jeong, Ji-Eun (Department of Pediatrics, School of Medicine, Catholic University of Daegu) ;
  • Lee, Kyung-Hun (Department of Pediatrics, School of Medicine, Catholic University of Daegu) ;
  • Sung, Hyun-Jung (Department of Pathology, School of Medicine, Catholic University of Daegu) ;
  • Cho, Chang-Ho (Department of Pathology, School of Medicine, Catholic University of Daegu)
  • 투고 : 2009.02.03
  • 심사 : 2009.02.27
  • 발행 : 2009.03.30
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초록

평소 복부 팽만을 보인 2세 남아가 내원 3일 전부터 간헐적인 구토를 동반하여 시행한 복부 방사선 사진에서 좌상복부에서 석회화 소견을 관찰하여 상부 위장관내시경과 복부 전산화 단층 사진을 시행하였다. 술 후 병리 검사에서 상당히 빈도가 드문 석회화 섬유 종양을 발견하였기에 보고하는 바이다.

Calcifying fibrous tumors (CFTs) are unusual benign tumors of childhood, located primarily in soft tissues, pleura, and peritoneum. The cause and pathogenesis are unclear. We report a rare case of a CFT in a 2-year-old boy who presented with vomiting and abdominal distension. An abdominal X-ray showed an elliptical, calcific shadow in the LUQ area mimicking a foreign body. An internally protruding mass along the lesser curvature of the gastric body was an incidental finding during upper endoscopy, biopsies of which were negative. Abdominal CT showed a 4.5${\times}$3.2 cm soft tissue mass of the gastric wall with calcifications. A diagnosis of gastric submucosal mass was suspected and a wedge resection of the stomach was performed. On microscopic examination, the tumor was composed of whorls of dense hyalinized collagen bundles with a few fibroblasts. There were also amorphous dystrophic calcifications and nodular aggregates of mononuclear inflammatory cells. Immunohistochemically, spindle cells did not stain for anaplastic lymphoma kinase-1 (ALK-1), CK, smooth muscle actin (SMA), or desmin. Taken together, the mass was compatible with a CFT of the gastric wall. This is the first reported case of CFT in a Korean child.

키워드

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