A Case of Primary Unclassified Spindle Cell Sarcoma of the Left Atrium

좌심방에 발생한 원발성 미분류 방추세포 육종 1례

  • Cho, Jeong-Hwan (Department of Internal Medicine, College of Medicine, Yeungnam University) ;
  • Hong, Geu-Ru (Department of Internal Medicine, College of Medicine, Yeungnam University) ;
  • Song, In-Wook (Department of Internal Medicine, College of Medicine, Yeungnam University) ;
  • Son, Chang-Woo (Department of Internal Medicine, College of Medicine, Yeungnam University) ;
  • Jung, Sun-Young (Department of Internal Medicine, College of Medicine, Yeungnam University) ;
  • Nam, Jong-Ho (Department of Internal Medicine, College of Medicine, Yeungnam University) ;
  • Kim, Mi-Jin (Department of Pathology, College of Medicine, Yeungnam University)
  • 조정환 (영남대학교 의과대학 내과학 교실) ;
  • 홍그루 (영남대학교 의과대학 내과학 교실) ;
  • 송인욱 (영남대학교 의과대학 내과학 교실) ;
  • 손창우 (영남대학교 의과대학 내과학 교실) ;
  • 정선영 (영남대학교 의과대학 내과학 교실) ;
  • 남종호 (영남대학교 의과대학 내과학 교실) ;
  • 김미진 (영남대학교 의과대학 병리학 교실)
  • Published : 2009.12.30

Abstract

Primary cardiac tumors are very uncommon. Seventy five percent of them are benign tumors and these are mostly myxomas. The malignant cardiac tumors, the majority of which are undifferentiated sarcomas, comprise up to 25% of all cardiac tumors. A primary malignant sarcoma of the myocardium is exceedingly rare. Thus, there have been very few such cases reported in the literature. We present here a case of a 15 year old man who had complaints of orthopnea and increasing exercise intolerance over a one month period. Transthoracic echocardiography demonstrated a well demarcated huge mass with left ventricular inflow obstruction on the posterior wall of the left atrium. The patient's symptoms were relieved by surgery. The histological diagnosis was an unclassified spindle cell sarcoma.

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