Journal of Chest Surgery

  • 제42권1호
  • /
  • Pages.92-95
  • /
  • 2009
  • /
  • 2765-1606(pISSN)
  • /
  • 2765-1614(eISSN)
대한심장혈관흉부외과학회 (The Korean Society for Thoracic and Cardiovascular Surgery)
권호 표지

심장에 국한된 유육종증 환자에서 시행된 심장 이식

Heart Transplantation Performed in a Patient with Isolated Cardiac Sarcoidosis

  • 조현진 (울산대학교 의과대학 서울아산병원 흉부외과학교실) ;
  • 정성호 (울산대학교 의과대학 서울아산병원 흉부외과학교실) ;
  • 윤태진 (울산대학교 의과대학 서울아산병원 흉부외과학교실) ;
  • 문덕환 (울산대학교 의과대학 서울아산병원 흉부외과학교실)
  • Cho, Hyun Jin (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Jung, Sung-Ho (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Yun, Tae-Jin (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Moon, Dukhwan (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine)
  • 투고 : 2008.07.23
  • 심사 : 2008.09.16
  • 발행 : 2009.02.05
PDF 다운로드
⟨ 이전 논문 다음 논문 ⟩

초록

유육종증은 면역 반응에 의한 전신 육아종성 염증 질환으로 20~60%에서 심장을 침범하는 것으로 알려져 있으나 심장에만 국한된 유육종증(Isolated cardiac sarcoidosis)은 매우 드물며, 전신 증상의 발현이 없는 제한된 경우에 심장 이식을 고려해 볼 수 있다. 저자들은 완전 방실 차단으로 영구형 심장 박동 조율기(Permanent pacemaker)를 삽입한 심장 유육종증 환자에서 스테로이드에 반응하지 않는 심부전의 악화로 심장 이식을 시행하였기에 보고하는 바이다.

Sarcoidosis is a systemic inflammatory disease with granulomatous lesions, and cardiac involvement occurs in 20~60% of patients. Isolated cardiac sarcoidosis is extremely rare, and heart transplantation can be performed, if indicated, contingent upon the absence of systemic manifestations of the disease. We present a case of isolated cardiac sarcoidosis with progressive heart failure, which was successfully managed by heart transplantation.

키워드

참고문헌

  1. Habersberger J, Manins V, Taylor AJ. Cardiac sarcoidosis. Intern Med J 2008;38:270-7 https://doi.org/10.1111/j.1445-5994.2007.01590.x
  2. Bargout R, Kelly RF. Sarcoid heart disease: clinical course and treatment. Int J Cardiol 2004;97:173-82 https://doi.org/10.1016/j.ijcard.2003.07.024
  3. Yazaki Y, Isobe M, Hiroe M, et al. Prognostic determinants of long-term survival in Japanese patients with cardiac sarcoidosis treated with prednisone. Am J Cardiol 2001;88: 1006-10 https://doi.org/10.1016/S0002-9149(01)01978-6
  4. Yoshida Y, Morimoto SI, Hiramitsu S, et al. Incidence of cardiac sarcoidosis in Japanese patients with high degree atrioventricular block. Am Heart J 1997;134:382-6 https://doi.org/10.1016/S0002-8703(97)70070-X
  5. Jang J, Min K, Jung GC, Kim J, Lee I. Cardiac sarcoidosis treated by cardiac transplantation: a case report. Korean J Pathol 2001;35:71-5
  6. Oni AA, Hershberger RE, Norman DJ, et al. Recurrence of sarcoidosis in a cardiac allograft: control with augmented corticosteroids. J Heart Lung Transplant 1992;11:367-9
  7. Yager JE, Hernandez AF, Steenbergen C, et al. Recurrence of cardiac sarcoidosis in a heart transplant recipient. J Heart Lung Transplant 2005;24:1988-90 https://doi.org/10.1016/j.healun.2005.02.016
  8. Zaidi AR, Zaidi A, Vaitkus PT. Outcome of heart transplantation in patients with sarcoid cardiomyopathy. J Heart Lung Transplant 2007;26:714-7 https://doi.org/10.1016/j.healun.2007.05.006