Heart Transplantation Performed in a Patient with Isolated Cardiac Sarcoidosis

심장에 국한된 유육종증 환자에서 시행된 심장 이식

  • Cho, Hyun Jin (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Jung, Sung-Ho (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Yun, Tae-Jin (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Moon, Dukhwan (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine)
  • 조현진 (울산대학교 의과대학 서울아산병원 흉부외과학교실) ;
  • 정성호 (울산대학교 의과대학 서울아산병원 흉부외과학교실) ;
  • 윤태진 (울산대학교 의과대학 서울아산병원 흉부외과학교실) ;
  • 문덕환 (울산대학교 의과대학 서울아산병원 흉부외과학교실)
  • Received : 2008.07.23
  • Accepted : 2008.09.16
  • Published : 2009.02.05

Abstract

Sarcoidosis is a systemic inflammatory disease with granulomatous lesions, and cardiac involvement occurs in 20~60% of patients. Isolated cardiac sarcoidosis is extremely rare, and heart transplantation can be performed, if indicated, contingent upon the absence of systemic manifestations of the disease. We present a case of isolated cardiac sarcoidosis with progressive heart failure, which was successfully managed by heart transplantation.

유육종증은 면역 반응에 의한 전신 육아종성 염증 질환으로 20~60%에서 심장을 침범하는 것으로 알려져 있으나 심장에만 국한된 유육종증(Isolated cardiac sarcoidosis)은 매우 드물며, 전신 증상의 발현이 없는 제한된 경우에 심장 이식을 고려해 볼 수 있다. 저자들은 완전 방실 차단으로 영구형 심장 박동 조율기(Permanent pacemaker)를 삽입한 심장 유육종증 환자에서 스테로이드에 반응하지 않는 심부전의 악화로 심장 이식을 시행하였기에 보고하는 바이다.

Keywords

References

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