Monostotic Fibrous Dysplasia in the Metacarpal Bone: A Case Report

중수골에 발생한 단골성 섬유성 이형성증: 1예 보고

  • Cho, Han-Il (Department of Radiology, Wonkwang University Hospital) ;
  • Park, Sung-Hoon (Department of Radiology, Wonkwang University Hospital) ;
  • Juhng, Seon-Kwan (Department of Radiology, Wonkwang University Hospital)
  • 조한일 (원광대학병원 영상의학과) ;
  • 박성훈 (원광대학병원 영상의학과) ;
  • 정선관 (원광대학병원 영상의학과)
  • Published : 2009.12.30

Abstract

Fibrous dysplasia is a slowly progressive, benign disorder characterized by fibrous tissue replacement of skeleton and may affect solitary or multiple bones. Monostotic fibrous dysplasia mainly occurrs in the rib, femur and tibia, however, rarely in the hand. We report a case of monostotic fibrous dysplasia confined to the 2nd metacarpal bone with findings of plain radiographs and MR imaging.

섬유성 이형성증은 원인불명의 섬유조직의 양성질환으로 정상적인 해면골이 섬유조직과 불규칙적인 골소주의 증식에 의해 점진적으로 대체되는 특징을 가지며 단골성 또는 다골성으로 발생한다. 단골성의 경우 주로 늑골, 대퇴골, 경골 등에서 흔히 발생하지만 손에 발생하는 경우는 매우 드문 것으로 알려져 있다. 저자들은 13세 남아의 중수골에 발생한 단골성 섬유성 이형성증의 단순X선촬영과 자기공명영상의 소견을 중심으로 증례보고 하고자 한다.

Keywords

References

  1. Lichtenstein L, Jaffe HL. Fibrous dysplasia of bone. Arch PathoI 1942;3:777-816
  2. Albright F. Syndromes characterized by osteitis fibrosa disseminata, areas of pigmentation and endocrine dysfunction with precocious puberty in female. N Engl J Med 1937;216:727-730 https://doi.org/10.1056/NEJM193704292161701
  3. Netherlands Committee. Fibrous dysplasia. In: Netherlands Committee, ed. Radiological atlas of bone tumours. Paris: Mouton and Co. 1973:479-500
  4. Schajowicz F. Fibrous dysplasia. In: Schajowicz F, ed. Tumors and tumor-like lesions of bone and joints. New York: Springer-Verlag 1981:478-490
  5. Milliez PY, Thomine JM. Rare benign bone tumors and dystrophy in the hand. Review of the literature and report of four cases. Ann Chit Main 1988;7:1125-1129
  6. Weaver AA. Monostotic fibrous dysplasia: a rare source of hand pain. A report of a case. Nebr Med J 1990;75 :43
  7. Hayter RG, Becton JL. Fibrous dysplasia of a metacarpal: a case report. J Hand Surg 1984;9A:587
  8. Fitzpatrick KA, Taljanovic MS, Speer DP et al. Imaging Findings of Fibrous Dysplasia with Histopathologic and Intraoperative Correlation. AJR Am J Roentgenol 2004;182:1389-1398 https://doi.org/10.2214/ajr.182.6.1821389
  9. Jee WH, Choi KH, Choe BY, Park JM, Shinn KS. Fibrous Dysplasia: MR Imaging Characteristics with Radiopathologic Correlation. AJR Am J Roentgenol 1996;167:1523-1527 https://doi.org/10.2214/ajr.167.6.8956590
  10. Yagoda MR, Selesnick SH. Temporal bone fibrous dysplasia and cholesteatoma leading to the developement of a parapharyngeal abscess. J Laryngol Otol 1994;108:51-53