Annals of Hepato-Biliary-Pancreatic Surgery (한국간담췌외과학회지)

The Korean Association of Hepato-Biliary-Pancreatic Surgery (한국간담췌외과학회)
권호 표지

Non-Functioning Somatostatinoma of the Duodenum in Patient with Von Recklinghausen's Disease

Von Recklinghausen's Disease 환자의 십이지장에 발생한 비기능성 Somatostatinoma 1예

  • Kim, Kang-Jae (Department of General Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Jang, Kee-Taek (Department of General Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Kim, Woo-Seok (Department of Pathology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Choi, Dong-Wook (Department of General Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine)
  • 김강재 (성균관대학교 의과대학 삼성서울병원 외과학교실) ;
  • 장기택 (성균관대학교 의과대학 삼성서울병원 외과학교실) ;
  • 김우석 (성균관대학교 의과대학 삼성서울병원 병리학교실) ;
  • 최동욱 (성균관대학교 의과대학 삼성서울병원 외과학교실)
  • Published : 2009.12.31

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Abstract

Somatostatinoma is a rare endocrine tumor that comprises around 1% of all gastroentero-pancreatic endocrine neoplasm. The estimated annual incidence is 1 in 40 million. This tumor may be associated with von Recklinghausen's disease. We present here a rare case of a 51-year-old female patient with a duodenal nonfunctioning somatostatinoma combined with von Recklinghausen's disease. Whipple' procedure was performed. The postoperative course was uneventful and the histopathologic findings were consistent with malignant nonfunctioning somatostatinoma with lymph node metastases. The patient is alive, healthy and without tumor recurrence 10 months after surgery.

Keywords

References

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