Lipoblastoma of Mediastinum - A case report -

종격동 지방모세포종 -1예 보고-

  • Cho, Jung-Soo (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Inha University) ;
  • Kim, Kwang-Ho (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Inha University) ;
  • Baek, Wan-Ki (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Inha University) ;
  • Kim, Joung-Taek (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Inha University) ;
  • Son, Byong-Kwan (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Inha University) ;
  • Kim, Won-Hong (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Inha University) ;
  • Kim, Lucia (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Inha University)
  • 조정수 (인하대학교 의과대학 흉부외과학교실) ;
  • 김광호 (인하대학교 의과대학 흉부외과학교실) ;
  • 백완기 (인하대학교 의과대학 흉부외과학교실) ;
  • 김정택 (인하대학교 의과대학 흉부외과학교실) ;
  • 손병관 (인하대학교 의과대학 흉부외과학교실) ;
  • 김원홍 (인하대학교 의과대학 흉부외과학교실) ;
  • 김루시아 (인하대학교 의과대학 흉부외과학교실)
  • Published : 2008.06.05

Abstract

Lipoblastoma is a rare benign tumor that usually originates in children from the embryonic lipid cells of the extremities. This condition shows an early childhood occurrence, a benign nature without metastasis, a cellular composition of mainly mature lipid cells and an ability to differentiate into a simple lipoma. We have experienced a 15 month old girl who had developed a lipoblastoma in the right anterior mediastinum. Surgical resection was carried out without complications. Her postoperative course was uneventful. She has been well 6 months after the operation.

지방모세포종은 상, 하지의 태생기 지방조직에서 기원하는 드문 양성 종양으로 영, 유아기에 주로 발생하며, 지방세포로 구성되어 있고 단순 지방종으로 분화되는 능력을 가지고 있는 것으로 알려져 있다. 본 종양이 종격동에 발생하는 경우는 매우 드문 것으로 알려져 있다. 저자들은 1년 3개월 된 여아에서 우측 전방 종격동에 발생된 지방모세포종을 치험하여 보고하는 바이다.

Keywords

References

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