소아에서 부승모판막(Accessoy Mitral Valve Tissue)에 의한 좌심실 유출로 협착 - 1예 보고 -

Left Ventricular Outflow Tract Obstruction Caused by Accessory Mitral Valve Tissue in a Child -A case report-

  • 이정은 (경상대학교 의과대학 흉부외과학교실, 경상대학교 건강과학원) ;
  • 이상호 (경상대학교 의과대학 흉부외과학교실, 경상대학교 건강과학원) ;
  • 최준영 (경상대학교 의과대학 흉부외과학교실, 경상대학교 건강과학원) ;
  • 양준호 (경상대학교 의과대학 흉부외과학교실, 경상대학교 건강과학원)
  • Lee, Chung-Eun (Department of Thoracic and Cardiovascular Surgery, Gyeongsang National University School of Medicine, Gyeongsang National University Institute of Health Sciences) ;
  • Lee, Sang-Ho (Department of Thoracic and Cardiovascular Surgery, Gyeongsang National University School of Medicine, Gyeongsang National University Institute of Health Sciences) ;
  • Choi, Jun-Young (Department of Thoracic and Cardiovascular Surgery, Gyeongsang National University School of Medicine, Gyeongsang National University Institute of Health Sciences) ;
  • Yang, Jun-Ho (Department of Thoracic and Cardiovascular Surgery, Gyeongsang National University School of Medicine, Gyeongsang National University Institute of Health Sciences)
  • 발행 : 2008.06.05

초록

부승모판막(accessory mitral valve tissue)은 매우 드문 선천성 심장병이며, 좌심실 유출로 협착(left ventricular outflow tract obstruction)의 드문 원인 중의 하나이다. 심수축기시에 부승모판막이 낙하산처럼 펴지며 잡아당기고 있어서 앞승모판막첨(anterior mitral valve leaflet)이 좌심실 유출로 쪽으로 당겨지면서 유출로 협착을 유발한다. 저자들은 본 환자에서 심초음파 검사를 통해 대동맥판막하 협착(subaortic stenosis)의 진단 하에 수술을 하였으며, 수술 중 부승모판막을 화인하고 수술을 하였기에 증례 보고를 하는 바이다.

Accessory mitral valve tissue is a very rare congenital cardiac malformation and it is an uncommon cause of left Ventricular outflow tract obstruction(LVOTO). The pathogenetic mechanism of subaortic obstruction is thought to be systolic ballooning of the abnormal valve tissue into LVOT. We are reporting a case of an accessory mitral valve tissue that was associated with LVOTO, and this was completely relieved after trans-aortic surgical excision of the accessory tissue.

키워드

참고문헌

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