A Case of Primary Mucinous Cystadenocarcinoma

원발성 후복막 점액낭샘암종 1예

Primary retroperitoneal mucinous cystadenocarcinoma is a very rare malignancy, and little is known concerning its pathogenesis, optimal treatment, and prognosis. A 29-year-old pregnant woman (21 weeks) presented with abdominal discomfort. CA 19-9, CA 125, and CEA were normal. Abdominal CT scanning revealed a $19{\times}15{\times}13cm$ retroperitoneal tumor. Exploratory laparotomy and tumor excision were performed. Mucinous retroperitoneal implants were removed as completely as possible. Histologically, the tumor showed focal areas of capsular invasion, but free resection margins. The uterus and both ovaries were normal in appearance. No adjuvant therapy was pursued. Six months later, peritoneal and bilateral ovarian metastases were discovered. Hence, we report the details of this case of primary retroperitoneal mucinous cystadenocarcinoma and present a review of the literature.

저자들은 임신 21주에 우하복부 종괴를 주소로 내원하여 원발성 후복막 점액성 낭성선암종으로 진단하고 종괴 적출술을 시행하였으나 수술 6개월 후 양측 난소 및 복막 전이를 보인 1예를 경험하였기에 보고하는 바이다.