Diffuse Dendriform Pulmonary Ossification with Spontaneous Pneumothorax

자발성 기흉을 동반한 미만성 수지상 폐 골화증

  • Cho, Hyun-Jin (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kim, Yong-Hee (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Park, Seung-Il (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kim, Dong-Kwan (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine)
  • 조현진 (울산대학교 의과대학 서울아산병원 흉부외과학교실) ;
  • 김용희 (울산대학교 의과대학 서울아산병원 흉부외과학교실) ;
  • 박승일 (울산대학교 의과대학 서울아산병원 흉부외과학교실) ;
  • 김동관 (울산대학교 의과대학 서울아산병원 흉부외과학교실)
  • Published : 2008.04.05

Abstract

Diffuse pulmonary ossification is a rare entity which was reported just a case in Korea, defined as "wide spread heterotropic bone formation within the lung parenchyme", and it's pathogenesis remains unclear. Generally, diffuse pulmonary ossification is diagnosed by autopsy because most of case is asymptomatic, and classified as either nodular and dendriform diagnosed pathologic examination. We reviewed a case of diffuse dendriform pulmonary ossification with spontaneous pneumothorax.

미만성 폐 골화증은 "폐실질 내에 발생하는 이소성 골 형성"으로 정의되는 매우 드문 질환으로 국내에서는 1예가 보고된 바 있으며, 발병 원인은 아직 뚜렷하게 밝혀지지 않았다. 일반적으로 미만성 폐 골화증은 무증상이어서 부검에 의해 진단되는 경우가 대부분이며, 조직 병리 소견에서 결절성과 수지상 두 가지로 분류된다. 저자들은 기존 질환의 병력이 없는 환자에서 발생한 자발성 기흉의 수술적 치료 후 조직 병리 검사에 의해 진단된 미만성 수지상 폐 골화증 1예를 보고하는 바이다.

Keywords

References

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