Pulmonary Langerhans Cell Histiocytosis Accompanied by Active Pulmonary Tuberculosis

활동성 폐결핵과 동반된 폐 랑거한스 세포 조직구증 - 1예 보고 -

  • Song, Dong-Seop (Department of Thoracic and Cardiovascular Surgery, Wonkwang University Sanbon Medical Center, Wonkwang University College of Medicine)
  • 송동섭 (원광대학교 의과대학 산본병원 흉부외과학교실)
  • Published : 2008.02.05

Abstract

Puimonary Langerhans cell histiocytosis is very rare, especially when accompanied by active pulmonary. tuberculosis. A patient was hospitalized due to excessive dyspnea and she was diagnosed with active pulmonary tuberculosis by a sputum AFB smear. The HRCT taken after hospitalization showed multiple micronodules and tiny cysts. An open lung biopsy confirmed the coexistence of pulmonary Langerhans cell histiocytosis.

폐 랑거한스 세포 조직구증은 랑거한스 세포 조직구증의 제한적 인 형태로 매우 드문 질환이다. 특히, 폐 랑거한스 세포 조직구증이 폐결핵과 동반되어 보고된 경우는 극히 드물다. 극심한 호흡곤란으로 입원한 환자가 객담 AFB 도말 검사로 활동성 폐결핵으로 진단되었다. 입원 후 시행한 고해상도 컴퓨터 단층 촬영에서 다수의 미세 결절과 작은 낭종들이 관찰되었다. 개흉 폐생검을 시행하였고 폐 랑거한스 세포 조직구증의 동반이 확인되었다.

Keywords

References

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