Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
권호 표지

Cardiac Rupture Induced by Angiosarcoma

혈관 육종에 의한 심장 파열

  • Choi, Jin-Ho (Department of Thoracic and Cardiovascular Surgery, Seoul National University College of Medicine) ;
  • Park, Kay-Hyun (Department of Thoracic and Cardiovascular Surgery, Seoul National University Bundang Hospital, Seoul National University College of Medicine) ;
  • Chung, Eui-Suk (Department of Thoracic and Cardiovascular Surgery, Seoul National University Bundang Hospital, Seoul National University College of Medicine) ;
  • Oh, Se-Jin (Department of Thoracic and Cardiovascular Surgery, Seoul National University College of Medicine) ;
  • Choi, Jin-Ho (Department of Thoracic and Cardiovascular Surgery, Seoul National University Bundang Hospital, Seoul National University College of Medicine) ;
  • Lim, Cheong (Department of Thoracic and Cardiovascular Surgery, Seoul National University Bundang Hospital, Seoul National University College of Medicine)
  • 최진호 (서울대학교 의과대학 흉부외과학교실) ;
  • 박계현 (서울대학교 의과대학 분당서울대학교병원 흉부외과학교실) ;
  • 정의석 (서울대학교 의과대학 분당서울대학교병원 흉부외과학교실) ;
  • 오세진 (서울대학교 의과대학 흉부외과학교실) ;
  • 최진호 (서울대학교 의과대학 분당서울대학교병원 흉부외과학교실) ;
  • 임청 (서울대학교 의과대학 분당서울대학교병원 흉부외과학교실)
  • Published : 2008.12.05
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Abstract

Angiosarcoma is the most common primary intracardiac malignancy, but many published papers have reported it to be rather rare. The prognosis of angiosarcoma is known to be very poor, and the treatment of choice has been surgery until recently, but many centers currently tend to try multi modal therapies, including chemotherapy and radiotherapy. In this report, we present a rare case in which an intracardiac angiosarcoma could have threatened the patient's life in short time by the rapid progression of the tumor, which caused right atrial rupture.

원발성 혈관육종은 매우 드물며 그 예후가 불량하다. 이전까지는 수술적 제거가 확립된 치료로 알려져 왔으나, 최근에는 수술 외에도 항암제 치료 및 방사선 치료 등을 병행하는 치료를 시도하고 있다. 저자들은 심장의 원발성 혈관육종의 빠른 진행으로 인하여 우심방의 파열을 일으켜 단시간 내에 환자의 사망을 일으킬 수도 있었던 드문 증례를 경험하여 보고하고자 한다.

Keywords

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