Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
권호 표지

Congenital Partial Pericardial Defect Presenting as Chest Pain

가슴 통증을 동반한 선천성 부분 심낭 결손증

  • Kim, Yong-Ho (Department of Thoracic and Cardiovascular Surgery, Chungnam National University Hospital, College of Medicine, Chungnam National University) ;
  • Kang, Min-Woong (Department of Thoracic and Cardiovascular Surgery, Chungnam National University Hospital, College of Medicine, Chungnam National University) ;
  • Lim, Seung-Pyung (Department of Thoracic and Cardiovascular Surgery, Chungnam National University Hospital, College of Medicine, Chungnam National University) ;
  • Lee, Young (Department of Thoracic and Cardiovascular Surgery, Chungnam National University Hospital, College of Medicine, Chungnam National University) ;
  • Gil, Hong-Ryang (Department of Pediatrics, Chungnam National University Hospital, College of Medicine, Chungnam National University) ;
  • Yu, Jae-Hyeon (Department of Thoracic and Cardiovascular Surgery, Chungnam National University Hospital, College of Medicine, Chungnam National University)
  • 김용호 (충남대학교 의과대학 충남대학교병원 흉부외과학교실) ;
  • 강민웅 (충남대학교 의과대학 충남대학교병원 흉부외과학교실) ;
  • 임승평 (충남대학교 의과대학 충남대학교병원 흉부외과학교실) ;
  • 이영 (충남대학교 의과대학 충남대학교병원 흉부외과학교실) ;
  • 길홍량 (충남대학교 의과대학 충남대학교병원 소아과학교실) ;
  • 유재현 (충남대학교 의과대학 충남대학교병원 흉부외과학교실)
  • Published : 2007.10.05
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Abstract

Patients with congenital pericardial defect display few symptoms and this is an unusual disease, so it is generally found incidentally in most of the cases. In some cases, symptoms such as chest pain are found due to partial cardiac herniation. We report here on a 14-year-old girl with dyspnea and chest pain that started during physical activity 3 months before the hospital visit. She was diagnosed with herniation of the left atrial appendage with a partial pericardium defect and she was treated with an operation.

심낭 결손증은 드문 선천성 기형으로 대부분의 경우 증상이 없이 우연히 발견되지만, 심장의 일부가 탈장되어 흉통 등의 증상을 나타내는 경우도 있다. 본 증례는 14세 여자 환자가 내원 3개월 전부터 발생한 운동 시 호흡곤란과 가슴 통증을 주소로 내원하여 부분 심낭 결손을 통한 좌심방 부속지의 탈장(herniation)이 진단되어 수술적 치료를 시행하여 보고하는 바이다.

Keywords

References

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