Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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A Case of Huge Pulmonary Blastoma With Multiorgan Invasion

다기관 침범을 동반한 거대 폐 모세포종

  • Lee, Tae Hwan (Department of Internal Medicine and Airway Remodeling Laboratory, Chonbuk National University Medical School) ;
  • Lee, Ka Young (Department of Internal Medicine and Airway Remodeling Laboratory, Chonbuk National University Medical School) ;
  • Kim, So Ri (Department of Internal Medicine and Airway Remodeling Laboratory, Chonbuk National University Medical School) ;
  • Min, Kyung Hun (Department of Internal Medicine and Airway Remodeling Laboratory, Chonbuk National University Medical School) ;
  • Park, Seoung Ju (Department of Internal Medicine and Airway Remodeling Laboratory, Chonbuk National University Medical School) ;
  • Lee, Heung Bum (Department of Internal Medicine and Airway Remodeling Laboratory, Chonbuk National University Medical School) ;
  • Rhee, Yang Keun (Department of Internal Medicine and Airway Remodeling Laboratory, Chonbuk National University Medical School) ;
  • Lee, Yong Chul (Department of Internal Medicine and Airway Remodeling Laboratory, Chonbuk National University Medical School)
  • 이태환 (기도 개형 연구실, 전북대학교 의과대학 내과학교실) ;
  • 이가영 (기도 개형 연구실, 전북대학교 의과대학 내과학교실) ;
  • 김소리 (기도 개형 연구실, 전북대학교 의과대학 내과학교실) ;
  • 민경훈 (기도 개형 연구실, 전북대학교 의과대학 내과학교실) ;
  • 박성주 (기도 개형 연구실, 전북대학교 의과대학 내과학교실) ;
  • 이흥범 (기도 개형 연구실, 전북대학교 의과대학 내과학교실) ;
  • 이양근 (기도 개형 연구실, 전북대학교 의과대학 내과학교실) ;
  • 이용철 (기도 개형 연구실, 전북대학교 의과대학 내과학교실)
  • Received : 2006.11.29
  • Accepted : 2006.12.27
  • Published : 2007.02.28
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Abstract

A pulmonary blastoma is a rare malignant tumor of the lung that is composed of epithelial and mesenchymal elements and resembles the structure of an embryonic lung. Pulmonary blastomas have a very poor prognosis and make up 0.25 to 0.5 percent of all primary malignant lung tumors. A pulmonary blastoma usually manifests as a solitary parenchymal mass or nodule and multiple subpleural mass with effusion on chest X-ray and computed tomography. We encountered a very rare case of pulmonary blastoma in a 52 years old male. He complained of abdominal pain, fullness, and dyspnea. The radiology examination revealed a huge lung mass invading the mediastinum, heart, diaphragm, and liver. The percutaneous needle biopsies were performed, and this tumor was diagnosed as a pulmonary blastoma. We report a biopsy confirmed case of a huge pulmonary blastoma invading multiple organs.

폐모세포종은 폐종양으로 매우 드물게 나타나며 드물게 간, 흉외 림프절, 심장으로 전이된다고 보고되고 있다. 본 저자들은 복부의 팽만감과 통증 및 호흡곤란을 주소로 내원한 환자에서 간과 폐의 거대 종괴를 발견하였고, 조직 검사를 통하여 간, 횡격막, 심장 등 다발성 침범을 동반한 폐모세포종으로 진단받은 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Keywords

References

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