Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Mediastinal Neurofibroma in a the Patient with Type 4 Neurofibromatosis -A case report-

피부 신경섬유종증을 동반한 환자에서의 종격동 신경섬유종 -1예 보고-

  • Lee, Jong-Ho (Department of Thoracic and Cardiovascular Surgery, Daejeon St. Mary's Hospital, The Catholic University of Korea College of Medicine) ;
  • Kwon, Jong-Bum (Department of Thoracic and Cardiovascular Surgery, Daejeon St. Mary's Hospital, The Catholic University of Korea College of Medicine) ;
  • Moon, Mi-Hyoung (Department of Thoracic and Cardiovascular Surgery, Kangnam St. Mary's Hospital, The Catholic University of Korea College of Medicine) ;
  • Park, Kuhn (Department of Thoracic and Cardiovascular Surgery, Daejeon St. Mary's Hospital, The Catholic University of Korea College of Medicine)
  • 이종호 (가톨릭대학교 의과대학 대전성모병원 흉부외과학교실) ;
  • 권종범 (가톨릭대학교 의과대학 대전성모병원 흉부외과학교실) ;
  • 문미형 (가톨릭대학교 의과대학 강남성모병원 흉부외과학교실) ;
  • 박건 (가톨릭대학교 의과대학 대전성모병원 흉부외과학교실)
  • Published : 2007.04.05
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Abstract

Neurogenic tumors are the most common posterior mediastinal tumors and accounting for $19{\sim}39%$ of all mediastinal tumors and 75% of all posterior mediastinal tumors. Neurofibromatosis is an autosomal dominant disorder with variable expression of tumors, including neurologic tumors of the peripheral nerves, nrve roots, and plexi. A posterior mediastinal neufibroma in neurofibromatosis patients is rare. We report here a case of posterior mediastinal neurofibroma in a patient with type 1 neurofibromatosis.

신경기원의 종양은 전체 종격동 종양의 $19{\sim}39%$를 차지하며 후종격동 종양의 75%를 차지하는 가장 흔한 종양이다. 신경섬유종증은 상염색체 우성으로 유전되는 질환으로 임상 양상은 다양하며, 신경계에서는 말초신경, 신경근, 신경총 등에서 종양을 형성한다. 신경섬유종증 환자에서의 후종격동 신경섬유종은 드물어, 이에 1형(type 1) 신경섬유종증 환자에서 후종격동에 발생한 신경섬유종을 경험하게 되어 보고한다.

Keywords

References

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