Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Desmoplastic Small Round Cell Tumor of the Mediastinum -A case report -

종격동에 발생한 결합조직형성 소원형세포 종양 - 1예 보고-

  • Kim, Jeong-Won (Department of Thoracic and Cardiovascular Surgery, Ulsan University Hospital, University of Ulsan College of Medicine) ;
  • Cha, Hee-Jeong (Department of Diagnostic Pathology, Ulsan University Hospital, University of Ulsan College of Medicine) ;
  • Park, Sang-Kyu (Department of Pediatrics, Ulsan University Hospital, University of Ulsan College of Medicine) ;
  • Jung, Jong-Pil (Department of Thoracic and Cardiovascular Surgery, Ulsan University Hospital, University of Ulsan College of Medicine) ;
  • Shin, Je-Kyoun (Department of Thoracic and Cardiovascular Surgery, Ulsan University Hospital, University of Ulsan College of Medicine) ;
  • Park, Chang-Ryul (Department of Thoracic and Cardiovascular Surgery, Ulsan University Hospital, University of Ulsan College of Medicine)
  • 김정원 (울산대학교 의과대학 울산대학교병원 흉부외과) ;
  • 차희정 (울산대학교 의과대학 울산대학교병원 병리과) ;
  • 박상규 (울산대학교 의과대학 울산대학교병원 소아과) ;
  • 정종필 (울산대학교 의과대학 울산대학교병원 흉부외과) ;
  • 신제균 (울산대학교 의과대학 울산대학교병원 흉부외과) ;
  • 박창률 (울산대학교 의과대학 울산대학교병원 흉부외과)
  • Published : 2007.02.05
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Abstract

Desmoplastic small round cell tumor (DSRCT) is rare and a recently described, poorly differentiated malignant tumor and it usually presents with widespread intra-abdominal involvement. We report a case of DSRCT arising form the mediastinum which was treated with multimodality anticancer therapy in 15 year-old girl.

결합조직형성 소원형세포 종양(desmoplastic small round cell tumor)은 최근에 발생 빈도가 증가하는 추세인 희귀한 종양으로 주로 복강 내에서 발생하는 것으로 알려져 있다. 저자들은 15세 여자 화자의 종격동에 발생한 결합조직형성 소원형세포 종양에 대해 적극적인 항암화학요법, 수술, 방사선치료 및 자가 말초혈 조혈모세포 이식 등의 복합요법으로 만족스러운 결과를 얻었기에 이를 국내 최초로 보고하고자 한다.

Keywords

References

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