Maxillofacial Plastic and Reconstructive Surgery

Korean Association of Maxillofacial Plastic and Reconstructive Surgeons (대한악안면성형재건외과학회)
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A CASE REPORT OF AMELOBLASTIC FIBROSARCOMA IN THE MANDIBLE

하악에 발생한 법랑아세포 섬유육종의 치험례

  • Yoon, Byong-Wook (Dept. of Oral & Maxillofacial Surgery, Kyung-Hee University Dental School) ;
  • Lee, Baek-Soo (Dept. of Oral & Maxillofacial Surgery, Kyung-Hee University Dental School) ;
  • Oh, Jung-Hwan (Dept. of Oral & Maxillofacial Surgery, Kyung-Hee University Dental School)
  • 윤병욱 (경희대학교 치의학전문대학원 구강악안면외과학교실) ;
  • 이백수 (경희대학교 치의학전문대학원 구강악안면외과학교실) ;
  • 오정환 (경희대학교 치의학전문대학원 구강악안면외과학교실)
  • Published : 2007.09.30
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Abstract

Ameloblastic fibrosarcoma(AFS) is a rare malignant odontogenic tumor presented as painful swelling and intraosseous mass with occasional ulceration. The most frequent site is the mandible body. AFS of the jaw generally occurs in all ages($3{\sim}83$ years old), with the average age of 27.3. AFS was associated with high local recurrence rate of 37% in the areas of gingiva, floor of mouth and neck. Although metastasis is not a special feature of this lesion, 20% have died within 3 months to 19 years, due to locally aggressive tumor growth. This report describes an ameloblastic fibrosarcoma occurring in the mandible of a twenty-five year old male. The tumor was treated by partial mandibulectomy and reconstructed with a fibular flap. The patient has shown no signs of recurrence or complications during 18 months postoperatively. In this study, we report our case with a review of literatures.

Keywords

References

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