Video-assisted Diaphragm Plication in Children with Diaphragm Eventration Associated with Congenital Myopathy - Report of 2 Cases -

선천성 근질환을 가진 횡격막 내장탈출 환아에서의 흉강경을 이용한 주름성형술 -2예 보고 -

  • Lee Jae-Hang (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine) ;
  • Kim Young-Tae (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine) ;
  • Kim Joo-Hyun (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine) ;
  • Kang Chang-Hyun (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine)
  • 이재항 (서울대학교병원 흉부외과, 서울대학교 의과대학 흉부외과학교실) ;
  • 김영태 (서울대학교병원 흉부외과, 서울대학교 의과대학 흉부외과학교실) ;
  • 김주현 (서울대학교병원 흉부외과, 서울대학교 의과대학 흉부외과학교실) ;
  • 강창현 (서울대학교병원 흉부외과, 서울대학교 의과대학 흉부외과학교실)
  • Published : 2006.09.01

Abstract

A six-month old boy and a thirty-month old girl who suffered from dyspnea were admitted to our hospital. Their primary disease was congenital myopathy, and both of them had a history of recurrent pneumonia. Chest X-ray scan showed unilateral diaphragmatic eventration. To minimize the injury of weakened respiratory muscle in children with myopathy, VATS plication was performed under double lung ventilation. Each of the two patients were discharged on the 17th and 24th postoperative day. We report two cases of successful VATS plication in children with diaphragmatic eventration associated with congenital myopathy.

6개월 남아와 30개월 여아가 호흡곤란을 주소로 내원하였다. 이들은 모두 선천성 근질환을 진단 받았으며 반복적인 폐렴의 과거력이 있었고 흉부방사선촬영상 횡격막성 내장탈출을 관찰할 수 있었다. 근질환을 가진 환아에 있어서 일반적인 개흉술을 시행할 경우 환아의 술 후 합병증의 발생 위험이 높다고 판단되어 흉강경을 이용한 주름성형술을 시행하였다. 두 환아는 각각 수술 후 17일, 24일째 퇴원하였으며 현재 외래에서 경과 관찰 중이다. 본원에서는 선천성 근질환을 가진 환아를 대상으로 흉강경을 이용한 주름성형술 2예를 체험하였기에 보고하는 바이다.

Keywords

References

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