Gastrointestinal Stromal tumor of the Esophagus

식도에 발생한 위장관 간질종양

  • Park Young-Woo (Department of Thoracic and Cardiovascular Surgery, Buchon Hospital, Soonchunyang University College of Medicine) ;
  • Shin Hwa-Kyun (Department of Thoracic and Cardiovascular Surgery, Buchon Hospital, Soonchunyang University College of Medicine) ;
  • Lim Jae-Ung (Department of Thoracic and Cardiovascular Surgery, Buchon Hospital, Soonchunyang University College of Medicine) ;
  • Koh Eun-Suk (Department of Clinical Pathology, Buchon Hospital, Soonchunyang University College of Medicine) ;
  • Kim Hee-Kyung (Department of Clinical Pathology, Buchon Hospital, Soonchunyang University College of Medicine) ;
  • Won Yong-Soon (Department of Thoracic and Cardiovascular Surgery, Buchon Hospital, Soonchunyang University College of Medicine)
  • 박영우 (순천향대학교 의과대학 부천병원 흉부외과) ;
  • 신화균 (순천향대학교 의과대학 부천병원 흉부외과) ;
  • 임재웅 (순천향대학교 의과대학 부천병원 흉부외과) ;
  • 고은석 (순천향대학교 의과대학 부천병원 임상병리과) ;
  • 김희경 (순천향대학교 의과대학 부천병원 임상병리과) ;
  • 원용순 (순천향대학교 의과대학 부천병원 흉부외과)
  • Published : 2006.07.01

Abstract

A 46-year-old man who had been diagnosed with esophageal tumor by PET-CT was admitted to our hospital for operation. Preoperative examination and intraoperative findings showed leiomyoma-like lesion and enucleation was done, but an immunohistochemical test on the case found gastrointestinal stromal tumor (GISTs). GISTs are very rarely found in the esophagus. As GISTs differ from leiomyoma pathogenetically and clinically, different treatments and follow-up strategies are required. The patient is under continuous observation to check recurrence and metastasis.

46세 남자환자가 건강검진에서 발견된 식도 종양을 수술받기 위해 내원하였다. 수술 전 검사 및 수술소견에서 평활근종과 유사한 소견을 보여 적출술을 시행하였으나 면역조직화학적 염색에서 위장관 간질종양으로 확인되었다. 식도에 발생하는 위장관 간질종양은 매우 드문 질환이다. 평활근종과는 다른 병리생물학적 소견과 임상양상을 보이므로 다른 치료방법 및 경과관찰이 필요하다. 환자는 재발 및 전이에 대한 지속적인 추적관찰 중이다.

Keywords

References

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