Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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A Case of Pulmonary Metastasis of a Dermatofibrosarcoma Protuberans

융기성 피부섬유육종의 폐전이 1예

  • Jung, Se Jin (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Byun, Min Kwang (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Chung, Woo Young (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Park, Moo Suk (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Kang, Shin Myung (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Kim, Hae Ryoung (Department of Pathology, Yonsei University College of Medicine) ;
  • Shin, Dong Hwan (The Institute of Chest Diseases, Yonsei University College of Medicine) ;
  • Kim, Se Kyu (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Chang, Joon (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Kim, Sung Kyu (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Kim, Young Sam (Department of Internal Medicine, Yonsei University College of Medicine)
  • 정세진 (연세대학교 의과대학 내과학교실) ;
  • 변민광 (연세대학교 의과대학 내과학교실) ;
  • 정우영 (연세대학교 의과대학 내과학교실) ;
  • 박무석 (연세대학교 의과대학 내과학교실,) ;
  • 강신명 (연세대학교 의과대학 내과학교실) ;
  • 김혜령 (연세대학교 의과대학 병리학교실) ;
  • 신동환 (연세대학교 의과대학 폐질환연구소) ;
  • 김세규 (연세대학교 의과대학 내과학교실) ;
  • 장준 (연세대학교 의과대학 내과학교실) ;
  • 김성규 (연세대학교 의과대학 내과학교실) ;
  • 김영삼 (연세대학교 의과대학 내과학교실)
  • Received : 2006.08.07
  • Accepted : 2006.10.11
  • Published : 2006.12.30
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Abstract

Dermatofibrosarcoma protuberans (DFPS) is a locally aggressive skin tumor with a very low incidence in the general population. This tumor has a remarkable tendency to recur, However, a metastasis is rare. We report a case of DFPS with a pulmonary metastasis in 28-year-old man. The pulmonary metastasis developed 5 years after a complete resection of the primary skin tumor. We reviewed the clinical manifestations and treatment of DFPS, and highlight the need for a long-term follow-up examination for metastases after a wide excision of these lesions.

저자들은 융기성 피부섬유육종을 완전 절제한 환자에서 5년 후에 원발부위에 재발없이 폐에 단독으로 전이된 1예를 경험하였기에 문헌 고찰과 함께 보고하는 바이다.

Keywords

References

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