Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Inflammatory Myofibroblastic Tumor of the Lung in a Child -A case report-

소아에시 발생한 폐 염증성 근섬유아세포종 -1예 보고-

  • Kim Hee-Jung (Department of Thoracic and Cardiovascular Surgery, Ulsan University Hospital, Ulsan University College of Medicine) ;
  • Park Chang-Ryul (Department of Thoracic and Cardiovascular Surgery, Ulsan University Hospital, Ulsan University College of Medicine) ;
  • Jung Jong-Pil (Department of Thoracic and Cardiovascular Surgery, Ulsan University Hospital, Ulsan University College of Medicine) ;
  • Shin Je-Kyoun (Department of Thoracic and Cardiovascular Surgery, Ulsan University Hospital, Ulsan University College of Medicine)
  • 김희중 (울산대학교 의과대학 울산대학교병원 흉부외과) ;
  • 박창률 (울산대학교 의과대학 울산대학교병원 흉부외과) ;
  • 정종필 (울산대학교 의과대학 울산대학교병원 흉부외과) ;
  • 신제균 (울산대학교 의과대학 울산대학교병원 흉부외과)
  • Published : 2006.04.01
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Abstract

Inflammatory myofbroblastic tumor in the lung is a rare tumor. The etiology is not clear. This tumor in children is a benign tumor rarely presented with local invasiveness, recurrence, distant metastasis or malignant changes can occur. The complete surgical resection is chosen as the optimal management. A 12-years-old boy visited the outpatient clinic with a 4 cm sized pulmonary mass in left upper lung field. The patient underwent left upper lobectomy. Histopathologically, inflammatory myofibroblastic tumor was confirmed. The patient was discharged without any problems and there was no evidence of recurrence during 3 months follow-up.

폐에서 발생하는 염증성 근섬유아세포종은 원인은 정확히 밝혀져 있지 않은 매우 드문 종양이다. 소아에서 발생한 이 종양은 양성종양으로 분류되어 있으나 드물게 국소침윤이나 재발, 원격전이 및 악성변이가 나타날 수 있다. 외과적 완전 절제술이 가장 적절한 치료 방법으로 되어 있다. 12세 남자가 단순흉부엑스선 사진에서 우연히 발견된 좌측 폐 상부의 4 cm크기의 응어리소견을 주소로 내원하였다. 환아는 좌상엽 절제수술을 받은 후 진단병리학적으로 염증성 근섬유아세포종으로 확진되었다. 환아는 술 후 3개월째 재발 소견없이 외래 추적 관찰 중이다.

Keywords

References

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