Experience of Single Stage Treatment of Caniosynostosis, Hypertelorism, Exophthalmos Patient

두개조기유합증, 안와격리증, 안구돌출증 환자의 동시 교정 치험례

  • Chung, Chul Hoon (Department of Plastic and Reconstructive Surgery, Hallym University College of Medicine) ;
  • Eun, Seok Chan (Department of Plastic and Reconstructive Surgery, Hallym University College of Medicine) ;
  • Seo, Dong Kuk (Department of Plastic and Reconstructive Surgery, Hallym University College of Medicine) ;
  • Jo, Woo Sung (Department of Plastic and Reconstructive Surgery, Hallym University College of Medicine) ;
  • Park, Se Hyuck (Department of Neurosurgery, Hallym University College of Medicine)
  • 정철훈 (한림대학교 의과대학 성형외과학교실) ;
  • 은석찬 (한림대학교 의과대학 성형외과학교실) ;
  • 서동국 (한림대학교 의과대학 성형외과학교실) ;
  • 조우성 (한림대학교 의과대학 성형외과학교실) ;
  • 박세혁 (한림대학교 의과대학 신경외과학교실)
  • Received : 2005.10.04
  • Published : 2006.03.10

Abstract

The simultaneous correction of the hypertelorism and exophthalmos combined with craniosynostosis is very rarely performed operative procedures in the world. The craniosynostosis is the congenital anomaly that designates premature fusion of one or more sutures in either cranial vault or cranial base. Hypertelorism is not a distinct clinical syndrome in itself, but is a physical finding secondary to facial and cranial maldevelopment and it is defined as a increase in the distance between the medial orbital walls. Exophthalmos can occur following the decrease in the size of the orbit in patients with developmental skeletal disorders such as craniofacial synostosis. The authors experienced 9-year-old male patient, who has complex cranio-facial abnormality. The craniosynostosis was oxycephaly type and primary fronto-orbital advancement surgery had been performed in other hospital. The abnormal cranial vault combined with hypertelorism and exophthalmos due to maldeveloped both orbital walls. Surgical correction was obtained by various cranio-fronto-orbital remodeling technique such as calvarial bone craniotomy, fronto-orbital advancement, paramedian resection, medial canthopexy, Tessier-Wolfe three wall orbital expansions. We achieved a quite satisfactory result both functionally and aesthetically in a complex cranio-facial deformity patient by combination and modification of previously developed various cranio-facial plasty technique and hereby report the case with brief discussion and review of literature.

Keywords

References

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