Clinical and Experimental Pediatrics

The Korean Pediatric Society (대한소아청소년과학회)
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A case of congenital ductus arteriosus aneurysm

Congenital ductus arteriosus aneurysm 1례

  • Wang, Sheng Wen (Department of Pediatrics, Dong-A University College of Medicine) ;
  • Kim, Ji Eun (Department of Pediatrics, Dong-A University College of Medicine) ;
  • Lee, Young Seok (Department of Pediatrics, Dong-A University College of Medicine) ;
  • Lee, Young Ah (Department of Pediatrics, Dong-A University College of Medicine)
  • 왕승문 (동아대학교 의과대학 소아과학교실) ;
  • 김지은 (동아대학교 의과대학 소아과학교실) ;
  • 이영석 (동아대학교 의과대학 소아과학교실) ;
  • 이영아 (동아대학교 의과대학 소아과학교실)
  • Received : 2006.07.18
  • Accepted : 2006.09.15
  • Published : 2006.12.15
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Abstract

Aneurysmal dilatation of the ductus arteriosis has been considered a rare but potentially fatal abnormality. The mechanism of ductal aneurysmal formation remains uncertain. Plain chest radiography has proven helpful in the diagnosis of ductus arteriosus aneurysm (DAA), before the application of transthoracic echocardiography. The transthoracic echocardiography is an important tool for the diagnosis and follow-up of DAA. We present a case of congenital ductus arteriosus aneurysm in a newborn, that was an incidental discovery. The diagnosis was made by echocardiography, three-dimensional surface rendering computed tomography (CT), and spontaneous regression after four weeks of follow-up.

신생아에서 흉강내 대동맥류는 드물며, 말판 증후군, 대동맥 축착, 대동맥 판막 협착, 동맥염, 터너 증후군, 결절성 경화증 등과 연관되어 보고된 바 있다. 신생아에서 발견되는 ductus arteriosus aneurysm은 매우 드문 질환이나, 대동맥 파열이 유발 될 수 있는 기형이다. 병인으로 대동맥 쪽에 있는 동맥관의 폐쇄 지연, 선천적으로 동맥관 벽이 약한 경우, 자궁내에서 동맥관으로 혈류 증가, 자궁내에서 동맥관의 협착 등이 있으나 명확하지 않은 상태이다. Ductus arteriosus aneurysm은 흉부 방사선, 심초음파, 3차원 전산화단층촬영, 자기 공명영상 검사 등으로 진단할 수 있다. 치료는 인도메사신의 투여, 수술적 절재 등의 방법이 있으며, 자연 소실되는 경우도 있다. 저자들은 태변흡인증후군 환아에서 우연히 발견된 ductus arteriosus aneurysm이 생후 4주 뒤 자연 소실되는 1례를 경험하였기에 보고하는 바이다.

Keywords

References

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