Hemifacial Pain Accompanied with Delayed Ipsilateral Abducens Nerve Palsy: Tolosa-Hunt Syndrome -A case report-

안면통에 동반된 가돌림신경의 지연 마비 증례: Tolosa-Hunt 증후군 -증례 보고-

  • Shim, Jae Kwang (Department of Anesthesiology and Pain Medicine Yonsei University College of Medicine) ;
  • Moon, Jin Cheon (Department of Anesthesiology and Pain Medicine Yonsei University College of Medicine) ;
  • Yoon, Kyung Bong (Department of Anesthesiology and Pain Medicine Yonsei University College of Medicine) ;
  • Kim, Won Oak (Department of Anesthesiology and Pain Medicine Yonsei University College of Medicine) ;
  • Yoon, Duck Mi (Department of Anesthesiology and Pain Medicine Yonsei University College of Medicine)
  • 심재광 (연세대학교 의과대학 마취통증의학교실) ;
  • 문진천 (연세대학교 의과대학 마취통증의학교실) ;
  • 윤경봉 (연세대학교 의과대학 마취통증의학교실) ;
  • 김원옥 (연세대학교 의과대학 마취통증의학교실) ;
  • 윤덕미 (연세대학교 의과대학 마취통증의학교실)
  • Received : 2006.01.03
  • Accepted : 2006.03.22
  • Published : 2006.06.30

Abstract

Tolosa-Hunt syndrome is a rare self-limiting disease that's characterized by painful ophthalmoplegia. It has a relapsing and remitting course, and the pain responds promptly to systemic corticosteroid therapy. Yet it is diagnosed by the exclusion of other major causes involving the superior orbital fissure or cavernous sinus, including trauma, neoplasm, aneurysm and inflammation. Further, the associated ophthalmoplegia may follow days to weeks after the onset of orbital or hemifacial pain. Hence, this condition is often misdiagnosed as atypical facial pain, and so improper management could result in unnecessary suffering of the patient. The following case describes a patient suffering with hemifacial pain associated with ipsilateral abducens nerve palsy, which was evident 2 weeks after the onset of pain, and this was misdiagnosed as trigeminal neuralgia and atypical facial pain.

Keywords

References

  1. Kline LB, Hoyt WF: The Tolosa-Hunt syndrome. J Neurol Neuro-surg Psychiatry 2001; 71: 577-82 https://doi.org/10.1136/jnnp.71.5.577
  2. Gladstone JP, Dodick DW: Painful ophthalmoplegia: overview with a focus on Tolosa-Hunt syndrome. Curr Pain Headache Rep 2004; 8: 321-9 https://doi.org/10.1007/s11916-004-0016-x
  3. La Mantia L, Etbetta A, Bussone G: Painful ophthalmoplegia: an untesolved clinical ptoblem. Neutol Sci 2005; 26: 79-82
  4. Motamed M, Kalan A: Gradenigo's syndrome. Postgtad Med J 2000; 76: 559-60 https://doi.org/10.1136/pmj.76.899.559
  5. Hunt WE, Meagher JN, LeFevet HE, Zeman W: Painful ophthalmoplegia. Its relation to indolent inflammation of the cavernous sinus. Neurology 1961; 11: 56-62 https://doi.org/10.1212/WNL.11.1.56
  6. Smith JL, Taxdal DS: Painful ophthalmoplegia. The Tolosa-Hunt syndrome. Am J Ophthalmol 1966; 61: 1466-72 https://doi.org/10.1016/0002-9394(66)90487-9
  7. Burston BJ, Ptetorius PM, Ramsden JD: Gradenigo's syndrome: successful conservative tteatment in adult and paediatric patients. J Latyngol Otol 2005; 119: 325-9
  8. Mathew NT, Chandy J: Painful ophthalmoplegia. J Neurol Sci 1970; 11: 243-56 https://doi.org/10.1016/0022-510X(70)90064-X
  9. Spinnler H: Painful ophthalmoplegia; the Tolosa-Hunt syndrome. Med J Aust 1973; 2: 645-6
  10. Headache Classification Subcommittee of the International Headache Society: The International classification of headache disorders 2nd ed. Cephalagia 2004; 24(suppl): 1-160
  11. Aron-Rosa D, Doyon D, Sallamon G, Michotey P: The Tolosa-Hunt syndrome. Ann Ophthalmol 1978; 10: 1161-8
  12. Kline LB: The Tolosa-Hunt syndrome. Surv Ophthalmol 1982; 27: 79-95 https://doi.org/10.1016/0039-6257(82)90190-4
  13. Cakirer S: MRI findings in Tolosa-Hunt syndtome before and after systemic corticostetoid therapy. Eur J Radiol 2003; 45: 83-90 https://doi.org/10.1016/S0720-048X(02)00012-8
  14. Jimene2-Caballero PE, Florensa J, Marsal-Alonso C, Alvarez-Tejerina A: Recurrent Tolosa-Hunt syndrome with notmal neuroimaging. A report of three cases. Rev Neurol 2005; 41: 30-3
  15. Foubert-Samiet A, Sibon I, Maite JP, Tison F: Long-term cure of Tolosa-Hunt syndrome after low-dose focal radiotherapy. Headache 2005; 45: 389-91 https://doi.org/10.1111/j.1526-4610.2005.05077_5.x
  16. Lee SS, Kim KS, Han YJ, Choi H: A case of unusual Tolosa-Hunt syndrome. Korean J Pain 1989; 2: 198-202