Archives of Plastic Surgery

Korean Society of Plastic and Reconstructive Surgeons (대한성형외과학회)
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A Large Malignant Peripheral Nerve Sheath Tumor in the Neurofibromatosis Patient: A Case Report

신경섬유종증 환자에 발생한 거대 악성말초신경초종의 치험례

  • Choi, Dong Il (Department of Plastic and Reconstructive Surgery, Hallym University) ;
  • Seo, Dong Kuk (Department of Plastic and Reconstructive Surgery, Hallym University) ;
  • Jo, Woo Sung (Department of Plastic and Reconstructive Surgery, Hallym University) ;
  • Chung, Chul Hoon (Department of Plastic and Reconstructive Surgery, Hallym University) ;
  • Cho, Seong Jin (Department of Pathology, College of Medicine, Hallym University)
  • 최동일 (한림대학교 의과대학 성형외과학교실) ;
  • 서동국 (한림대학교 의과대학 성형외과학교실) ;
  • 조우성 (한림대학교 의과대학 성형외과학교실) ;
  • 정철훈 (한림대학교 의과대학 성형외과학교실) ;
  • 조성진 (한림대학교 의과대학 해부병리학교실)
  • Received : 2006.04.07
  • Published : 2006.11.10
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Abstract

Purpose: Malignant peripheral nerve sheath tumors most often arise from the anatomically discernible peripheral nerve or neurofibroma. Methods: A 55-year-old man had a rapidly growing pedunculated large mass on the sacrolumbar junction for 2 years. He has congenital neurofibromatosis type I. He had multiple caf-au-lait spots and multiple neurofibromas on the entire body. The mass developed from a subcutaneous nodule on the sacrolumbar junction and grew rapidly. The preoperative punch biopsy revealed a malignant peripheral nerve tumor. The mass was completely excised with 1 cm free margin above the deep fascial plane. Results: There was no evidence of recurrence of tumor for 19 months of follow-up examination. Conclusion: Malignant peripheral nerve sheath tumor is very rare and has unique feature. We report a successful case of malignant peripheral nerve sheath tumor with the review of the literatures.

Keywords

References

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