Primary leiomyosarcoma presenting as a rapidly enlarging gingival mass of the mandible

하악 치은에 발생한 원발성 평활근육종

  • Cho, Bong-Hae (Department of Oral and maxillofacial Radiology, College of Dentistry, Pusan National University) ;
  • Nah, Kyung-Soo (Department of Oral and maxillofacial Radiology, College of Dentistry, Pusan National University) ;
  • Jung, Yun-Hoa (Department of Oral and maxillofacial Radiology, College of Dentistry, Pusan National University)
  • Published : 2006.12.31

Abstract

Leiomyosarcoma of the oral cavity is a very rare tumor that is associated with aggressive clinical behavior and low survival. In this paper, we report a case of leiomyosarcoma presenting with a gingival exophytic mass that rapidly grew, causing facial asymmetry within 16 days, in a 9-year-old boy. After an excisional biopsy, microscopy revealed a spindle cell neoplasm that, on immunohistochemistry analysis, demonstrated reactivity for SMA. This established the diagnosis of leiomyosarcoma; subsequently, a marginal mandibulectomy and supraomohyoid neck dissection were performed.

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