A Case Report of Restrictive Ventricular Septal Defect & Left Ventricular Out Flow Tract Stenosis Caused by Fibrotic Tissue in Tetralogy of Fallot

섬유성 조직으로 인한 제한적 심실 중격 결손과 좌심실 유출로 협착을 보인 활로씨 4증 1예 보고

  • Hwang, Ui-Dong (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Jung, Sung-Ho (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Seo, Dong-Man (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine)
  • 황의동 (울산대학교 의과대학 서울아산병원 흉부외과) ;
  • 정성호 (울산대학교 의과대학 서울아산병원 흉부외과) ;
  • 서동만 (울산대학교 의과대학 서울아산병원 흉부외과)
  • Published : 2006.11.05

Abstract

The VSD in TOF is usually large and unrestrictive with an equal to or greater than that of the aortic annulus. Typically shunting through the VSD is bidirectional or right-to-left component. Restrictive VSD in TOF caused by ingrowing fibrotic tissue is very rare. We report a case of restrictive VSD and LVOTO in TOF caused by ingrowing fibrotic tissue with the review of literature.

일반적으로 활로씨 4증에서의 심실 중격 결손은 보통 대동맥 판막륜의 크기와 같거나 크고 제한적이지 않다. 또한 심실 중격 결손을 통한 단락의 방향은 양방향성 또는 우-좌 단락인 경우가 대부분이다. 이러한 활로씨 4증에서 섬유성 조직의 성장으로 인한 제한적 심실 중격 결손은 드물게 보고되고 있다. 저자들은 활로씨 4증에서의 섬유성 조직으로 인한 제한적 심실 중격 결손과 좌심실 유출로 협착을 보였던 환아에 대한 완전 교정술 치험 1예를 문헌 고찰과 함께 보고한다.

Keywords

References

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