Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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A Case of Epithelioid Hemangioendothelioma Involving the Lung, Pleura and Liver

흉막과 간을 동시에 침범한 폐의 유상피 혈관내피종 1예

  • Na, Joo Ock (Department of Internal Medicine, Soonchunhyang University Collage of Medicine) ;
  • Seo, Ki Hyun (Department of Internal Medicine, Soonchunhyang University Collage of Medicine) ;
  • Park, Ji Young (Department of Internal Medicine, Soonchunhyang University Collage of Medicine) ;
  • Kim, Jung Hoon (Department of Internal Medicine, Soonchunhyang University Collage of Medicine) ;
  • Kim, Tae Hoon (Department of Internal Medicine, Soonchunhyang University Collage of Medicine) ;
  • Choi, Jae Sung (Department of Internal Medicine, Soonchunhyang University Collage of Medicine) ;
  • Kim, Yong Hoon (Department of Internal Medicine, Soonchunhyang University Collage of Medicine)
  • 나주옥 (순천향대학교 의과대학 내과학교실) ;
  • 서기현 (순천향대학교 의과대학 내과학교실) ;
  • 박지영 (순천향대학교 의과대학 내과학교실) ;
  • 김정훈 (순천향대학교 의과대학 내과학교실) ;
  • 김태훈 (순천향대학교 의과대학 내과학교실) ;
  • 최재성 (순천향대학교 의과대학 내과학교실) ;
  • 김용훈 (순천향대학교 의과대학 내과학교실)
  • Received : 2004.11.29
  • Accepted : 2005.01.18
  • Published : 2005.02.28
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Abstract

Epithelioid hemangioendothelioma (EH) is a rare borderline malignant tumor which originating from vascular endothelial cells and occurs in many organs such as soft tissues, lung, liver and bone. But, pulmonary EH which simultaneously involves pleura and liver is very rare. In the present report, we describe an uncommon case of EH involving the lung, pleura and liver in a 26-year-old woman. Chest CT showed single nodule in right upper lobe with large amount of pleural effusion at ipsilateral side and abdominal CT multiple round low densities in liver. The EH was confirmed by microscopic analysis and immunohistochemical staining of CD34+ from open lung biopsy specimen.

폐의 유상피 혈관 내피종이 진단 당시 흉막과 간을 동시에 침범한 경우는 드물다. 저자 등은 폐에 결절이 있고 동측에 다량의 흉막 삼출액이 동반되어 있으면서 간에 다발성 결절을 보인 26세의 젊은 여자환자에서 개흉 폐생검으로 진단된 유상피 혈관내피종 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Keywords

References

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