사지의 강직을 주소로 내원한 호산구성 근막염 환자

A Case of Eosinophilic Fasciitis Presenting as Stiffness of all Limbs

  • 허재혁 (서울대학교 의과대학 신경과학교실) ;
  • 민주홍 (서울대학교 의과대학 신경과학교실) ;
  • 권형민 (서울대학교 의과대학 신경과학교실) ;
  • 김지영 (서울대학교 의과대학 신경과학교실) ;
  • 조중양 (인제대학교 의과대학 일산백병원 신경과) ;
  • 이광우 (서울대학교 의과대학 신경과학교실)
  • Heo, Jae-Hyeok (Department of Neurology, College of Medicine, Seoul National University) ;
  • Min, Ju-Hong (Department of Neurology, College of Medicine, Seoul National University) ;
  • Kwon, Hyung-Min (Department of Neurology, College of Medicine, Seoul National University) ;
  • Kim, Ji-Young (Department of Neurology, College of Medicine, Seoul National University) ;
  • Cho, Joong-Yang (Department of Neurology, Ilsan Paik Hospital, College of Medicine, Inje University) ;
  • Lee, Kwang-Woo (Department of Neurology, College of Medicine, Seoul National University)
  • 발행 : 2005.05.31

초록

Eosinophilic fasciitis (EF), also known as Shulman syndrome, is an inflammatory disorder of unknown etiology. It usually presents with pain, swelling, and tenderness of the proximal aspect of the limbs, chest, or neck, with subsequent induration of the skin and subcutaneous tissues, in association with peripheral eosinophilia. EF is differentiated from scleroderma by the pattern of skin involvement and non-involvement of muscle. We report a case of progressive EF presented with tightness and stiffness in all limbs.

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