Annals of Clinical Neurophysiology
- 제7권1호
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- Pages.37-42
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- 2005
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- 2508-691X(pISSN)
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- 2508-6960(eISSN)
비전형적인 중상으로 발현한 급성 출혈성 백질뇌염
Atypical Manifestation of Acute Hemorrhagic Leukoencephalitis (Hurst's Disease)
- 민주홍 (서울대학교병원 신경과) ;
- 이수호 (서울대학교병원 신경과) ;
- 조중양 (인제대학교 일산백병원 신경과) ;
-
박성혜
(서울대학교병원 병리과) ;
- 이광우 (서울대학교병원 신경과)
- Min, Ju-Hong (Department of Neurology, Seoul National University Hospital, College of Medicine, Seoul National University) ;
- Lee, Su-Ho (Department of Neurology, Seoul National University Hospital, College of Medicine, Seoul National University) ;
- Cho, Joong-Yang (Department of Neurology, Ilsan Paik Hospital, College of Medicine, Inje University) ;
-
Park, Sung-Hye
(Department of pathology, Seoul National University Hospital, College of Medicine, Seoul National University) ;
- Lee, Kwang-Woo (Department of Neurology, Seoul National University Hospital, College of Medicine, Seoul National University)
- 발행 : 2005.05.31
초록
Acute disseminated encephalomyelitis (ADEM) and acute hemorrhagic leukoencephalitis (Hurst's disease) are rare autoimmune demyelinating disorders, which show a monophasic illness with preceding infection. We report a 42-year-old woman presented with multiphasic and progressive neurologic deterioration without definite evidences of infection. She developed hypesthetic ataxia, followed by ipsilateral weakness after a weak, and finally encephalopathy after a month. In contrast to the first MRI showing a small longitudinal lesion, the next images revealed massive bilateral frontal lesions with hemorrhagic necrosis and biopsy unveiled inflammatory demyelination.