급성 염증성 탈수초성 다발성 신경병의 임상 양상을 보인 IgA λ형 Monoclonal Gammopathy of Undetermined Significance 1례

A Case of IgA λ Monoclonal Gammopathy of Undetermined Significance Mimicking Acute Inflammatory Demyelinating Polyradiculoneuropathy

  • 이영배 (가천의과대학교 길병원 신경과학교실) ;
  • 전성호 (가천의과대학교 길병원 신경과학교실) ;
  • 한동철 (가천의과대학교 길병원 신경과학교실) ;
  • 신동진 (가천의과대학교 길병원 신경과학교실)
  • Lee, Yeong-Bae (Department of Neurology, Ghil Medical Center, Gachon Medical school) ;
  • Jeon, Seong-Ho (Department of Neurology, Ghil Medical Center, Gachon Medical school) ;
  • Han, Dong-Chul (Department of Neurology, Ghil Medical Center, Gachon Medical school) ;
  • Shin, Dong-Jin (Department of Neurology, Ghil Medical Center, Gachon Medical school)
  • 발행 : 2005.05.31

초록

Polyneuropathy that is associated with monoclonal gammopathy of undetermined significance (MGUS) similar to chronic inflammatory demyelinating polyneuropathy (CIDP) has been reported before, whereas a connection to acute inflammatory demyelinating polyneuropathy (AIDP) has not been. A 52 year-old man was presented with ascending paralysis beginning 1 day ago. Neurological examinations showed facial diplegia and decreased motor power and deep tendon reflexes in all extremities. On electrophysiologic study, sensorimotor polyneuropathy was observed. Protein-and immunoelectrophoresis revealed IgA $\lambda$ monoclonal gammopathy. High dose steroid therapy was given and the symptoms improved slightly.

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