Journal of Korean Neurosurgical Society

The Korean Neurosurgical Society (대한신경외과학회)
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Malignant Transformation of Fibrous Dysplasia on Anterior Skull Base

  • Lee, Chul-Jae (Department of Neurosurgery, Kosin University College of Medicine) ;
  • Kim, Seong-Min (Department of Neurosurgery, Eulji University School of Medicine)
  • Published : 2005.05.28
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Abstract

Malignant transformation of fibrous dysplasia is a rare condition and the incidence is estimated at 0.4% for fibrous dysplasia and 4% for Albright's syndrome. The authors did not find a reported case of malignant change at skull base around the orbit in the literature. We experienced a case of fibrous dysplasia, in which neurologic symptoms were aggravated due to malignant change around the orbit, and report its favorable outcome obtained with total surgical removal.

Keywords

References

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