Journal of Korean Neurosurgical Society

The Korean Neurosurgical Society (대한신경외과학회)
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Atypical Teratoid Rhabdoid Tumors in Adult Patient with Multiple Lesions

  • Oh, Young-Min (Department of Neurosurgery, Research Institute of Clinical Medicine, Chonbuk National University Medical School and Hospital) ;
  • Koh, Eun-Jeong (Department of Neurosurgery, Research Institute of Clinical Medicine, Chonbuk National University Medical School and Hospital) ;
  • Choi, Ha-Young (Department of Neurosurgery, Research Institute of Clinical Medicine, Chonbuk National University Medical School and Hospital)
  • Published : 2005.11.28
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Abstract

Primary atypical teratoid/rhabdoid tumor[AT/RT] of the central nervous system is a recently described, highly malignant neoplasm that usually occur in the posterior fossa of children. Although AT/RT usually occurs in young children, AT/RT is being recognized in adults with increasing frequency. The authors report 49-year-old man with multiple AT/RT lesions [right lateral ventricle, right temporal lobe and right cerebellum]. Histopathologic findings showed typical rhabdoid cells with eccentric nuclei and prominent nucleoli. Eventhough the tumor was removed, a patient was dead in one month after surgery due to recurrence and rapid regrowth of the tumor.

Keywords

References

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