Clinical and Experimental Pediatrics

대한소아청소년과학회 (The Korean Pediatric Society)
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대동맥류를 초래한 식도 중복 1례

A Life-Threatening Case of Tubular Esophageal Duplication Complicated with Aneurysm of the Aorta

  • 정연경 (대구가톨릭대학교 의과대학 소아과학교실) ;
  • 이경훈 (대구가톨릭대학교 의과대학 소아과학교실) ;
  • 정혜리 (대구가톨릭대학교 의과대학 소아과학교실) ;
  • 박기성 (대구가톨릭대학교 의과대학 흉부외과학교실) ;
  • 정경재 (대구가톨릭대학교 의과대학 방사선과학교실) ;
  • 조창호 (대구가톨릭대학교 의과대학 병리학교실)
  • Jung, Yeon Kyung (Departments of Pediatrics, School of Medicine, Catholic University of Daegu) ;
  • Lee, Gyeong Hoon (Departments of Pediatrics, School of Medicine, Catholic University of Daegu) ;
  • Chung, Hai Lee (Departments of Pediatrics, School of Medicine, Catholic University of Daegu) ;
  • Park, Ki Sung (Departments of Cardiothoracic Surgery, School of Medicine, Catholic University of Daegu) ;
  • Jung, Kyung-Jae (Departments of Radiology, School of Medicine, Catholic University of Daegu) ;
  • Cho, Chang Ho (Departments of Pathology, School of Medicine, Catholic University of Daegu)
  • 투고 : 2004.12.20
  • 심사 : 2005.03.04
  • 발행 : 2005.06.15
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초록

저자들은 발열과 끙끙거림을 주소로 내원한 2개월 된 소아에서 빈도가 드문 선천성 식도 중복의 감염, 파열로 인하여 농흉, 유미흉과 종격동염을 초래하고 이로 인하여 대동맥류를 초래한 1례를 경험하였기에 보고하고자 한다. 본 증례의 희귀함과 종격동염, 농흉, 대동맥류와 같은 다양한 합병증의 발생은 식도 중복을 진단하는데 있어서 어려운 점이었다.

Esophageal duplication cysts are rare congenital lesions that occur as a result of a failure in the tubulation of the esophagus. They are most frequently single, tubular, or cystic. They may cause compressive symptoms or may be discovered incidentally on chest radiographs. They become symptomatic when complications develop. Symptoms often are related to the location of the duplication; esophageal lesions can create respiratory difficulties. The definitive diagnosis of esophageal duplication cysts requires the pathological evaluation of the cyst after surgical removal. We experienced a rare tubular esophageal duplication, in a 2-month old girl who presented with fever and grunting. This is the first reported case in which the sequence of events of ruptured tubular esophageal duplication with empyema, mediastinitis and aneurysm occured.

키워드

참고문헌

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