Clinical and Experimental Pediatrics

The Korean Pediatric Society (대한소아청소년과학회)
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A Case of Protein Losing Enteropathy Associated with Henoch-Schönlein Purpura

Henoch-Schönlein 자반증에서 발생된 단백소실장증 1례

  • Kim, Kee Dae (Department of Pediatrics, St. Benedict Hospital, Busan) ;
  • Oh, Chang Whan (Department of Pediatrics, St. Benedict Hospital, Busan) ;
  • Lee, Eun Young (Department of Pediatrics, St. Benedict Hospital, Busan) ;
  • Kim, Jae Young (Department of Pediatrics, St. Benedict Hospital, Busan)
  • Received : 2004.09.15
  • Accepted : 2004.10.12
  • Published : 2005.02.15
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Abstract

Henoch-$Sch{\ddot{o}}nlein$ purpura(HSP) is an IgA mediated immune complex vasculitic disease characterized by non-thrombocytic purpura, arthritis, gastrointestinal manifestations, and glomerulonephritis. HSP related glomerulonephritis induces hypoproteinemia and edema in some cases. Protein-losing enteropathy is another rare but known manifestation of HSP leading to hypoproteinemia and edema. We report a 6-year-old girl with HSP who showed edema caused by intestinal protein loss, evidenced by elevated fecal alpha 1 antitrypsin clearance.

Henoch-$Sch{\ddot{o}}nlein$ 자반증에서 복통과 혈변이 가장 흔한 위장관계 침범 증상이며, 주요 위장관계 합병증은 발생빈도가 매우 낮다. 특히 국내 소아에서 단백소실장증이 합병된 보고 예는 아직까지 없다. 저자들은 Henoch-$Sch{\ddot{o}}nlein$ 자반증에서 경과 중에 단백소실장증이 합병된 6세 여아를 경험하였기에 문헌고찰과 함께 보고한다.

Keywords

References

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