Treatment of Mediastinal Growing Teratoma Syndrome - A case report -

종격동에 발생한 성장 기형종 증후군(Growing Teratoma Syndrome)의 치험 -1예 보고-

  • Cho Jong Ho (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Korea University) ;
  • Son Ho Sung (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Korea University) ;
  • Jo Won Min (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Korea University) ;
  • Min Byoung Ju (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Korea University) ;
  • Lee In Sung (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Korea University) ;
  • Shin Jae Seung (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Korea University)
  • 조종호 (고려대학교 의과대학 흉부외과학교실) ;
  • 손호성 (고려대학교 의과대학 흉부외과학교실) ;
  • 조원민 (고려대학교 의과대학 흉부외과학교실) ;
  • 민병주 (고려대학교 의과대학 흉부외과학교실) ;
  • 이인성 (고려대학교 의과대학 흉부외과학교실) ;
  • 신재승 (고려대학교 의과대학 흉부외과학교실)
  • Published : 2005.10.01

Abstract

A 15-year-old male was admitted with right-sided chest pain and cough for one month. On chest computed tomographic scan, a $10\times15\times16$ em-sized huge mediastinal mass was occupied in the right hemithorax. Radiologically, it seemed that the tumor was severely adhesive on the heart and the superior vena cava. Therefore we decided on chemotherapy and radiotherapy first instead of surgery. The tumor marker was nearly normalized afterwards, but the tumor size was seemed to be bigger on chest tomographic scan. This suggests the growing teratoma syndrome. After the successful resection, he showed symptomatic improvement and is being followed up without any symptoms in an out patient department up to now.

특이 병력 없던 15세 남자가 내원 한 달 전부터 시작된 우측 흉통과 함께 기침을 호소하여 본원 응급실로 내원하였다. 흉부 전산화 단층촬영에서 $10\times15\times16cm$크기의 전 종격동 종양으로 상대 정맥과 심장을 압박하면서 침범하고 있는 소견을 보였다. 수술 절제가 불가능한 것으로 판단하여 항암 및 방사선 치료를 시행하였다. 이후 종양 표지자는 거의 정상화되었으나 오히려 종양의 크기가 증가하는 소견을 보여, 종격동의 성장 기형종 증후군(Mediastinal Growing Teratoma Syndrome)으로 판단되어 수술을 시도하였다. 종양의 수술적 제거 후 환자는 24개월째 잔존 종양 및 재발 없이 외래 관찰 중이다.

Keywords

References

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