선천성 기관 협착 환자의 기관성형술 2예

Tracheoplasty for Congenital Tracheal Stenosis-Two case reports-

  • 임홍국 (부천세종병원 흉부외과, 세종심장연구소) ;
  • 이창하 (부천세종병원 흉부외과, 세종심장연구소) ;
  • 황성욱 (부천세종병원 흉부외과, 세종심장연구소) ;
  • 이철 (부천세종병원 흉부외과, 세종심장연구소) ;
  • 김재현 (부천세종병원 흉부외과, 세종심장연구소) ;
  • 서홍주 (부천세종병원 흉부외과, 세종심장연구소) ;
  • 정성철 (부천세종병원 흉부외과, 세종심장연구소)
  • Lim Hong Gook (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute) ;
  • Lee Chang-Ha (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute) ;
  • Hwang Seong Wook (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute) ;
  • Lee Cheul (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute) ;
  • Kim Jae Hyun (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute) ;
  • Seo Hong Joo (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute) ;
  • Jung Sung Chol (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
  • 발행 : 2005.08.01

초록

선천성 기관 협착증은 드문 질환이며, 장분절성 기관 협착은 아주 치명적이다. 신생아나 영아에서 심한 호흡 부전이 발생하고 복합 심기형이 동반되면 수술 교정이 쉽지 않다. 선천성 심기형을 동반한 장분절성 기관 협착으로 인공 호흡기 이탈이 불가능한 2.6 kg 체중의 어린 영아 1예와 신생아 1예에 서 기관성형술을 시행하였다. 심실중격결손증 수술 후 미만성 기관 협착이 발견된 어린 영아는 기관 절제술 및 좌측 주 기관지로의 확장 문합술을 시행받았으며, 미만성 근위부 기관 협착과 팔로사징을 동반한 신생아는 활주 기관성형술과 팔로사징 완전 교정술을 동시에 시행받았다. 두 환아 모두 술후 컴퓨터 단층 촬영에서 양호한 결과를 보였으며, 현재 증상 없이 건강한 상태이다.

Congenital tracheal stenosis can be a life-threatening disease, especially in cases involving the long-segment of the trachea. When patients are symptomatic immediately after birth or develop an accompanying complex cardiac anomaly, surgical repair can be a considerable challenge. We experienced a tracheoplasty in one early infant weighing 2.6 kg and one neonate who had ventilator dependency from long-segment congenital tracheal stenosis and congenital cardiac anomaly. One early infant, who had diffuse stenosis of distal trachea after ventricular septal defect closure, underwent resection and extended end to end anastomosis. One neonate who had diffuse stenosis of proximal trachea with tetralogy of Fallot (TOF), underwent slide tracheoplasty with total correction for TOF Postoperative chest computed tomography showed widely patent trachea. Both infants are now well without symptoms.

키워드

참고문헌

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