Childhood Kidney Diseases

Korean Society of Pediatric Nephrology (대한소아신장학회)
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Distal Renal Tubular Acidosis Complicated with Periodic Hypokalemic Paralysis

원위 신세뇨관성 산증에 합병된 급성 주기성 저칼륨혈증 마비 1례

  • Park Jee-Min (Department of Pediatrics, The Institute of Kidney Disease, Yonsei University College of Medicine) ;
  • Noh Byoung-Ho (Department of Pediatrics, The Institute of Kidney Disease, Yonsei University College of Medicine) ;
  • Shin Jae-Il (Department of Pediatrics, The Institute of Kidney Disease, Yonsei University College of Medicine) ;
  • Kim Myung-Jun (Department of Diagnostic Radiology, Yonsei University College of Medicine) ;
  • Lee Jae-Seung (Department of Pediatrics, The Institute of Kidney Disease, Yonsei University College of Medicine)
  • 박지민 (연세대학교 의과대학 소아과학교실, 신장질환연구소) ;
  • 노병호 (연세대학교 의과대학 소아과학교실, 신장질환연구소) ;
  • 신재일 (연세대학교 의과대학 소아과학교실, 신장질환연구소) ;
  • 김명준 (연세대학교 의과대학 진단방사선과학교실) ;
  • 이재승 (연세대학교 의과대학 소아과학교실, 신장질환연구소)
  • Published : 2004.04.01
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Abstract

A 5-year-old girl was admitted because of an acute onset of weakness in her extremities. She had experienced a similar episode before but had recovered spontaneously. She had previously been diagnosed with distal renal tubular acidosis(RTA) at the age of 2 months. During the period of acute paralysis, her serum potassium level was 1.8 mmol/L and the muscle enzymes were markedly raised suggesting massive rhabdomyolysis. Although hypokalemia is common in renal tubular acidosis, acute paralytic presentation is uncommon and is rarely described in children. We report a case of distal RTA complicated with hypokalemic paralysis with a brief review of related literatures.

저자들은 생후 2개월에 신석회화증, 원위 신세뇨관성 산증을 진단받고 지속적인 외래 추적 관찰을 하고 있는 여아에서 급성 저칼륨혈증 주기성 마비를 진단하였기에 문헌 고찰과 함께 보고하는 바이다.

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