Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Intravenous Leiomyomatosis Extending into Right Ventricle Association with Pulmonary Metastasis

폐전이를 동반한 우심실까지 확장된 정맥내 평활근종증

  • 이해영 (고신대학교 의과대학 흉부외과학교실) ;
  • 조봉균 (고신대학교 의과대학 흉부외과학교실) ;
  • 김종인 (고신대학교 의과대학 흉부외과학교실) ;
  • 변정훈 (고신대학교 의과대학 흉부외과학교실) ;
  • 천봉권 (고신대학교 의과대학 병리학교실) ;
  • 조성래 (고신대학교 의과대학 흉부외과학교실)
  • Published : 2004.11.01
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Abstract

Intravenous leiomyomatosis is a rare disease entity of benign smooth muscle invading into the lumen of veins. We describe a case of intravenous leiomyomatosis originating from the uterus, growing in the inferior vena cava, and extending into the right ventricle association with multiple pulmonary metastasis. A 53-year-old woman with chest discomfort and several times attacks of syncope was treated at our hospital. The tumor was successfully removed with moderate hypothermic cardiopulmonary bypass after total hysterectomy with a bilateral salphingo-oophorectomy, and multiple pulmonary metastasis under simultaneous sternotomy and laparotomy was confirmed.

정맥내 평활근종증은 자궁근육이나 혈관벽에서 발생한 평활근종이 정맥로를 통해 확장되어, 조직학적으로는 양성이나 임상적으로는 악성 경과를 취하는 매우 드문 질환이다. 종양은 대부분 정맥을 통로로 하공정맥, 우심방, 우심실, 심지어 폐동맥까지 확장되어 우심장의 폐쇄를 일으키면서 증상을 나타내는 것으로 되어 있으나, 매우 드물게 폐전이도 일으키는 것으로 보고되고 있다. 자궁에서 발생한 정맥내 평활근종이 우심실까지 확장되어 우심 폐쇄의 증상과 폐전이를 일으킨 53세의 여자 환자를 수술 치험하였기에 문헌고찰과 함께 보고한다.

Keywords

References

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