성인에서 발견된 선천성 낭성 선종양기형 1예

A Case of Congenital Cystic Adenomatoid Malformation(CCAM) of the Lung in Adult

  • 조용선 (을지대학교 의과대학 내과학교실) ;
  • 이양덕 (을지대학교 의과대학 내과학교실) ;
  • 한민수 (을지대학교 의과대학 내과학교실) ;
  • 강동욱 (을지대학교 의과대학 병리학교실)
  • Cho, Yongsoen (Department of Internal Medicine, School of Medicine, Eulji University) ;
  • Lee, Yang Duk (Department of Internal Medicine, School of Medicine, Eulji University) ;
  • Han, Minsoo (Department of Internal Medicine, School of Medicine, Eulji University) ;
  • Kang, Tong Uk (Department of Pathology, School of Medicine, Eulji University)
  • 발행 : 2003.07.30

초록

A congenital cystic adenoid malformation of the lung(CCAM) is characterized by an anomalous fetal development of the terminal respiratory structures, resulting in the adenomatoid proliferation of the bronchiolar elements and cystic formation. CCAM has been detected on the fetus, premature babies and stillborn as well as infants and children. An adult presentation of CCAM is extremely rare. When cystic lesions occur with a repeated infection, an evaluation of the cystic lesions requires a differential diagnosis of CCAM, sequestration, a lung abscess, a pneumatocele and a bronchogenic cyst. The definite treatment of CCAM is the surgical removal of the involved lobe. We report a case of a CCAM in a 24-year-old female with a brief review of the relevant literature.

키워드