Tuberculosis and Respiratory Diseases
- 제54권2호
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- Pages.230-235
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- 2003
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- 1738-3536(pISSN)
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- 2005-6184(eISSN)
원발성 폐동맥 육종 1례
A Case of Primary Pulmonary Artery Sarcoma
- 김희정 (가톨릭대학교 의과대학 내과학교실) ;
- 서석민 (가톨릭대학교 의과대학 내과학교실) ;
- 김성용 (가톨릭대학교 의과대학 내과학교실) ;
- 김명숙 (가톨릭대학교 의과대학 내과학교실) ;
- 김승준 (가톨릭대학교 의과대학 내과학교실) ;
-
김영균
(가톨릭대학교 의과대학 내과학교실)
;
- 김관형 (가톨릭대학교 의과대학 내과학교실) ;
- 문화식 (가톨릭대학교 의과대학 내과학교실) ;
- 송정섭 (가톨릭대학교 의과대학 내과학교실) ;
- 박성학 (가톨릭대학교 의과대학 내과학교실)
- Kim, Hee Joung (Department of Internal Medicine, Kangnam St. Mary's Hospital, The Catholic University of Korea) ;
- Seo, Suk Min (Department of Internal Medicine, Kangnam St. Mary's Hospital, The Catholic University of Korea) ;
- Kim, Sung Yong (Department of Internal Medicine, Kangnam St. Mary's Hospital, The Catholic University of Korea) ;
- Kim, Myung Sook (Department of Internal Medicine, Kangnam St. Mary's Hospital, The Catholic University of Korea) ;
- Kim, Seung Joon (Department of Internal Medicine, Kangnam St. Mary's Hospital, The Catholic University of Korea) ;
-
Kim, Young Kyoon
(Department of Internal Medicine, Kangnam St. Mary's Hospital, The Catholic University of Korea)
;
- Kim, Kwan Hyoung (Department of Internal Medicine, Kangnam St. Mary's Hospital, The Catholic University of Korea) ;
- Moon, Hwa Sik (Department of Internal Medicine, Kangnam St. Mary's Hospital, The Catholic University of Korea) ;
- Song, Jeong Sup (Department of Internal Medicine, Kangnam St. Mary's Hospital, The Catholic University of Korea) ;
- Park, Sung Hak (Department of Internal Medicine, Kangnam St. Mary's Hospital, The Catholic University of Korea)
- 발행 : 2003.02.28
초록
저자들은 폐색전증 의심하에 항응고제를 포함한 약물치료를 시행하였으나 임상증상의 호전이 없는 환자에서, 흉부 전산화단층촬영과 흉부 자기공명영상촬영을 통해 색전을 동반한 혈관의 종물을 발견한 후 수술적 제거로 진단한 원발성 폐동맥 육종 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.
A primary pulmonary artery sarcoma is a rare malignant tumor derived from the intimal layer of the pulmonary artery. Its clinical presentation can lead to a misdiagnosis of more common diseases such as thromboembolic disease. It is known to have a very poor prognosis. Therefore, the correct diagnosis of a primary pulmonary artery sarcoma is difficult and often delayed. We experienced a case of primary pulmonary artery sarcoma mimicking a pulmonary thromboembolism. The patient was admitted as a result of progressive dyspnea and coughing. The lung perfusion scan showed a large perfusion defect involving almost the entire right lung and suspicious small perfusion defects in the left upper lobe. Magnetic resonance imaging of the chest showed an enhancing nodule within the thrombus in the right pulmonary artery. The mass was removed completely by surgery, but the patient died as a result of shock.