Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Primary Pulmonary Angiosarcoma Presenting as Enbodronchial Stenosis -One Case Report

기관지 협착을 동반한 원발성 폐동맥 육종 -1예 보고-

  • 김경화 (전북대학교 의과대학 흉부외과학교실) ;
  • 서연호 (전북대학교 의과대학 흉부외과학교실) ;
  • 김민호 (전북대학교 의과대학 흉부외과학교실)
  • Published : 2003.10.01
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Abstract

Primary pulmonary angiosarcomas are extremely rare tumors. The diagnosis is often delayed due to nonspecific symptoms, mimicking pulmonary embolism and require careful clinical evaluation to exclude metastasis from the heart, pericardium, and distant extrathoracic sites. Most diagnosis are made postmortem. We report a case of primary pulmonary angiosarcoma histopathologically confirmed postoperatively, which was clinically suspected endobronchial carcinoma with endobronchial obstruction with relavant literature review.

원발성 폐동맥 육종은 매우 드문 질환이다 비특이적인 다양한 임상증상과 폐동맥 색전증 등으로 혼돈할 수도 있어 진단이 매우 어렵고, 지연될 수가 있다. 드물지만 원발성 육종이 호발하는 심장, 심막에서의 전이유무나 혹은 원격 전이에 대해서도 주의를 기울여야 한다. 저자들은 기관지 협착을 동반한 원발성 폐동맥 육종에 대해 수술 1예를 경험하였기에 문헌 고찰과 함께 보고하고자 한다.

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References

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