Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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One-stage Repair of Truncus Arteriosus with Interrupted Arch

대동맥궁 차단증를 동반한 동맥간의 일차 완전교정 - 1예 보고-

  • 성시찬 (부산대학교 의과대학 흉부외과학교실) ;
  • 박준호 (부산대학교 의과대학 흉부외과학교실) ;
  • 이형두 (부산대학교 의과대학 소아과학교실) ;
  • 김시호 (동아대학교 의과대학 흉부외과학교실) ;
  • 우종수 (동아대학교 의과대학 흉부외과학교실) ;
  • 이영석 (동아대학교 의과대학 소아과학교실)
  • Published : 2003.10.01
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Abstract

Truncus arteriosus with interrupted aortic arch is a very rare congenital cardiac anomaly that has an unfavorable natural course. We report a successful one-stage repair of truncus arteriosus with interrupted aortic arch through median sternotomy in a 25-day-old neonate weighing 3.1 kg. We reconstructed the aortic arch with direct side-to-end anastomosis between ascending and descending aortas. The right ventricular outflow reconstruction was performed with untreated autologous pericardial conduit without valve following Lecompte maneuver. The patient has been grown-up in good condition (25 ∼ 50 percentile of body weight) and shows the right ventricular outflow tract wide 1 year after the operation.

대동맥궁 차단증을 동반한 동맥간은 매우 중한 자연경과를 갖고 있는 희귀한 선천성 심장 기형이다. 생후 25일,체중 3.1 kg의 신생아에서 정중흉골절개술에 의한 일차 완전교정술을 시행하였다. A형 대동맥궁 차단증은 하행대동맥을 원위부 상행대동맥에 직접 문합하였으며, 폐동맥을 동맥간으로부터 분리하여 동맥간의 앞쪽에 위치한 다음 처리하지 않은 무판막 자가심낭도관을 사용하여 우심실 유출로를 재건하였다. 성공적 교정술 후 약 1년간의 양호한 추적결과를 경험하였기에 보고하는 바이다.

Keywords

References

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