피부병변없이 간질성 폐섬유화로 표현된 경피증 1례

A Case of Systemic Sclerosis Sine Scleroderma Presenting as Pulmonary Interstitial Fibrosis

  • 곽진호 (계명대학교 의과대학 내과학교실) ;
  • 최원일 (계명대학교 의과대학 내과학교실) ;
  • 이승현 (계명대학교 의과대학 내과학교실) ;
  • 서창균 (계명대학교 의과대학 내과학교실) ;
  • 김경찬 (계명대학교 의과대학 내과학교실) ;
  • 김민수 (계명대학교 의과대학 내과학교실) ;
  • 권건영 (계명대학교 의과대학 해부병리학교실) ;
  • 서수지 (계명대학교 의과대학 진단방사선학교실) ;
  • 박창권 (계명대학교 의과대학 흉부외과학교실) ;
  • 전영준 (계명대학교 의과대학 내과학교실)
  • Kwak, Jin-Ho (Department of Internal Medicine, Keimyung University School of Medicine) ;
  • Choi, Won-II (Department of Internal Medicine, Keimyung University School of Medicine) ;
  • Lee, Seung-Hyun (Department of Internal Medicine, Keimyung University School of Medicine) ;
  • Seo, Chang-Gyun (Department of Internal Medicine, Keimyung University School of Medicine) ;
  • Kim, Kyung-Chan (Department of Internal Medicine, Keimyung University School of Medicine) ;
  • Kim, Min-Su (Department of Internal Medicine, Keimyung University School of Medicine) ;
  • Kwon, Kun-Young (Department of Pathology, Keimyung University School of Medicine) ;
  • Suh, Soo-Ji (Department of Diagnostic Radiology, Keimyung University School of Medicine) ;
  • Park, Chang-Kwon (Department of Thoracic and Cardiovascular Surgery, Keimyung University School of Medicine) ;
  • Jeon, Young-June (Department of Internal Medicine, Keimyung University School of Medicine)
  • 발행 : 2001.04.30

초록

저자들은 4개월간의 호흡곤란을 주소로 내원하여 피부병변은 없었지만 흉강경하 폐생검과 식도내압검사, 핵항체검사 등으로 경피증을 확진한 Systemic sclerosis sine scleroderma 1례를 경험하였기에 문헌 고찰과 함께 보고하는 바이다.

Lung involvement in systemic sclerosis(SSC) is common but usually occurs late in the course. Skin changes usually occur before the pulmonary findings. In this report, a patient who developed pulmonary interstitial fibrosis without skin changes is presented. A diagnosis of SSC lung involvement was made histologically. The a nti-scl-70 antibody test was positive. Esophageal manometry revealed a lower amplitude in the lower two-third of the esophagus and pressure in the lower esophageal sphincter. Here we report a case of systemic sclerosis sine scleroderma presenting as pulmonary interstitial fibrosis with a review of the relevant literatures.

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