Tuberculosis and Respiratory Diseases
- Volume 50 Issue 4
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- Pages.493-498
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- 2001
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- 1738-3536(pISSN)
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- 2005-6184(eISSN)
A Case of Systemic Sclerosis Sine Scleroderma Presenting as Pulmonary Interstitial Fibrosis
피부병변없이 간질성 폐섬유화로 표현된 경피증 1례
- Kwak, Jin-Ho (Department of Internal Medicine, Keimyung University School of Medicine) ;
- Choi, Won-II (Department of Internal Medicine, Keimyung University School of Medicine) ;
- Lee, Seung-Hyun (Department of Internal Medicine, Keimyung University School of Medicine) ;
- Seo, Chang-Gyun (Department of Internal Medicine, Keimyung University School of Medicine) ;
- Kim, Kyung-Chan (Department of Internal Medicine, Keimyung University School of Medicine) ;
- Kim, Min-Su (Department of Internal Medicine, Keimyung University School of Medicine) ;
- Kwon, Kun-Young (Department of Pathology, Keimyung University School of Medicine) ;
- Suh, Soo-Ji (Department of Diagnostic Radiology, Keimyung University School of Medicine) ;
- Park, Chang-Kwon (Department of Thoracic and Cardiovascular Surgery, Keimyung University School of Medicine) ;
- Jeon, Young-June (Department of Internal Medicine, Keimyung University School of Medicine)
- 곽진호 (계명대학교 의과대학 내과학교실) ;
- 최원일 (계명대학교 의과대학 내과학교실) ;
- 이승현 (계명대학교 의과대학 내과학교실) ;
- 서창균 (계명대학교 의과대학 내과학교실) ;
- 김경찬 (계명대학교 의과대학 내과학교실) ;
- 김민수 (계명대학교 의과대학 내과학교실) ;
- 권건영 (계명대학교 의과대학 해부병리학교실) ;
- 서수지 (계명대학교 의과대학 진단방사선학교실) ;
- 박창권 (계명대학교 의과대학 흉부외과학교실) ;
- 전영준 (계명대학교 의과대학 내과학교실)
- Published : 2001.04.30
Abstract
Lung involvement in systemic sclerosis(SSC) is common but usually occurs late in the course. Skin changes usually occur before the pulmonary findings. In this report, a patient who developed pulmonary interstitial fibrosis without skin changes is presented. A diagnosis of SSC lung involvement was made histologically. The a nti-scl-70 antibody test was positive. Esophageal manometry revealed a lower amplitude in the lower two-third of the esophagus and pressure in the lower esophageal sphincter. Here we report a case of systemic sclerosis sine scleroderma presenting as pulmonary interstitial fibrosis with a review of the relevant literatures.
저자들은 4개월간의 호흡곤란을 주소로 내원하여 피부병변은 없었지만 흉강경하 폐생검과 식도내압검사, 핵항체검사 등으로 경피증을 확진한 Systemic sclerosis sine scleroderma 1례를 경험하였기에 문헌 고찰과 함께 보고하는 바이다.