Pulmonary Lymphangioleiomyomatosis with Chylous Pleural Effusion

유미흉수를 동반한 폐 임파관 평활근종증 1예

  • Park, Byong-Joon (Department of Internal medicine, Inha University College of medicine) ;
  • Cho, Jae-Hwa (Department of Internal medicine, Inha University College of medicine) ;
  • Moon, Tae-Hoon (Department of Internal medicine, Inha University College of medicine) ;
  • Park, Sang-Joon (Department of Internal medicine, Inha University College of medicine) ;
  • Ryu, Jung-Seon (Department of Internal medicine, Inha University College of medicine) ;
  • Lee, Hong-Lyeol (Department of Internal medicine, Inha University College of medicine) ;
  • Kwak, Seung-Min (Department of Internal medicine, Inha University College of medicine) ;
  • Cho, Chul-Ho (Department of Internal medicine, Inha University College of medicine)
  • 박병준 (인하대학교 의과대학 내과학교실) ;
  • 조재화 (인하대학교 의과대학 내과학교실) ;
  • 문태훈 (인하대학교 의과대학 내과학교실) ;
  • 박상준 (인하대학교 의과대학 내과학교실) ;
  • 류정선 (인하대학교 의과대학 내과학교실) ;
  • 이홍렬 (인하대학교 의과대학 내과학교실) ;
  • 곽승민 (인하대학교 의과대학 내과학교실) ;
  • 조철호 (인하대학교 의과대학 내과학교실)
  • Published : 2001.01.30

Abstract

Pulmonary lymphangioleiomyomatosis is a disease involving the proliferation of atypical smooth muscle cells from the perilymphatics, peribronchial and perivascular region of the lung and the retroperitneum. The disease usually affects women of child-bearing age. We recently experienced a case of pulmonary lymphangioleiomyomatosis in a 31-year-old women who had suffered from a chylous pleural effusion. Histologic confirmation of lymphangioleiomyomatosis Was made upon a video-associated thoracoscopic lung biopsy. Here we report this case with a brief review of the literature.

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